4.1.1.37: uroporphyrinogen decarboxylase
This is an abbreviated version!
For detailed information about uroporphyrinogen decarboxylase, go to the full flat file.
Word Map on EC 4.1.1.37
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4.1.1.37
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porphyria
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cutanea
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tarda
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heme
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erythrocyte
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porphyrinogenic
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hexachlorobenzene
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urinary
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hepatoerythropoietic
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porphobilinogen
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overload
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photosensitivity
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ferrochelatase
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protoporphyrin
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hemochromatosis
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5-aminolaevulinate
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heptacarboxylic
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hexachlorobenzene-induced
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hypertrichosis
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phlebotomy
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erythropoietic
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delta-aminolaevulinic
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polyhalogenated
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5-aminolevulinic
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protoporphyrinogen
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uroporphyria
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tetrapyrrole
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sun-exposed
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blister
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siderosis
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diagnostics
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3,4,3\',4\'-tetrachlorobiphenyl
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medicine
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hcb-induced
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miliae
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coproporphyria
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bulla
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agriculture
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hepta
- 4.1.1.37
- porphyria
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cutanea
- tarda
- heme
- erythrocyte
-
porphyrinogenic
- hexachlorobenzene
- urinary
-
hepatoerythropoietic
- porphobilinogen
- overload
-
photosensitivity
-
ferrochelatase
- protoporphyrin
- hemochromatosis
-
5-aminolaevulinate
-
heptacarboxylic
-
hexachlorobenzene-induced
- hypertrichosis
-
phlebotomy
-
erythropoietic
-
delta-aminolaevulinic
-
polyhalogenated
-
5-aminolevulinic
- protoporphyrinogen
-
uroporphyria
- tetrapyrrole
-
sun-exposed
- blister
- siderosis
- diagnostics
-
3,4,3\',4\'-tetrachlorobiphenyl
- medicine
-
hcb-induced
-
miliae
- coproporphyria
- bulla
- agriculture
-
hepta
Reaction
Synonyms
ch-UroD, Decarboxylase, uroporphyrinogen, Hem12p, PCL, Porphyrinogen carboxy-lyase, rl-UroD, tobacco UROD, UORO-D, UPD, URO-D, Uro-decarboxylase, uro-III decarboxylase, UroD, UROD protein, UROD1, uroporphyrinogen decarboxylase, uroporphyrinogen decarboxylase 1, Uroporphyrinogen III decarboxylase, uroporphyrinogen-decarboxylase, uroporphyrinogen-III decarboxylase
ECTree
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Specific Activity
Specific Activity on EC 4.1.1.37 - uroporphyrinogen decarboxylase
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additional information
additional information
recombinant mutant A22V substrate uroporphyrinogen-I, 62.6% of recombinant wild-type activity
additional information
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recombinant mutant A22V substrate uroporphyrinogen-I, 62.6% of recombinant wild-type activity
additional information
recombinant mutant A22V substrate uroporphyrinogen-III, 73.2% of recombinant wild-type activity
additional information
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recombinant mutant A22V substrate uroporphyrinogen-III, 73.2% of recombinant wild-type activity
additional information
recombinant mutant F84I substrate uroporphyrinogen-I, 1.7% of recombinant wild-type activity
additional information
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recombinant mutant F84I substrate uroporphyrinogen-I, 1.7% of recombinant wild-type activity
additional information
recombinant mutant F84I substrate uroporphyrinogen-III, 2.3% of recombinant wild-type activity
additional information
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recombinant mutant F84I substrate uroporphyrinogen-III, 2.3% of recombinant wild-type activity
additional information
recombinant mutant T141I substrate uroporphyrinogen-I, 21.3% of recombinant wild-type activity
additional information
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recombinant mutant T141I substrate uroporphyrinogen-I, 21.3% of recombinant wild-type activity
additional information
recombinant mutant T141I substrate uroporphyrinogen-III, 26.7% of recombinant wild-type activity
additional information
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recombinant mutant T141I substrate uroporphyrinogen-III, 26.7% of recombinant wild-type activity
additional information
recombinant mutant Y182C substrate uroporphyrinogen-I, 40.0% of recombinant wild-type activity
additional information
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recombinant mutant Y182C substrate uroporphyrinogen-I, 40.0% of recombinant wild-type activity
additional information
recombinant mutant Y182C substrate uroporphyrinogen-III, 65.2% of recombinant wild-type activity
additional information
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recombinant mutant Y182C substrate uroporphyrinogen-III, 65.2% of recombinant wild-type activity
additional information
recombinat mutant G318R substrate uroporphyrinogen-I 60.9 percent of recombinant wild-type
additional information
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recombinat mutant G318R substrate uroporphyrinogen-I 60.9 percent of recombinant wild-type
additional information
recombinat mutant G318R substrate uroporphyrinogen-III 76.2 percent of recombinant wild-type
additional information
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recombinat mutant G318R substrate uroporphyrinogen-III 76.2 percent of recombinant wild-type
additional information
recombinat mutant K297N substrate uroporphyrinogen-I 63.1 percent of recombinant wild-type
additional information
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recombinat mutant K297N substrate uroporphyrinogen-I 63.1 percent of recombinant wild-type
additional information
recombinat mutant K297N substrate uroporphyrinogen-III 73.7 percent of recombinant wild-type
additional information
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recombinat mutant K297N substrate uroporphyrinogen-III 73.7 percent of recombinant wild-type
additional information
subnormal uroporphyrinogen decarboxylase activity results in accumulation and urinary excretion of uroporphyrin and heptacarboxyl porphyrin
additional information
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subnormal uroporphyrinogen decarboxylase activity results in accumulation and urinary excretion of uroporphyrin and heptacarboxyl porphyrin