2.4.1.47: N-acylsphingosine galactosyltransferase
This is an abbreviated version!
For detailed information about N-acylsphingosine galactosyltransferase, go to the full flat file.
Word Map on EC 2.4.1.47
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2.4.1.47
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myelin
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oligodendrocyte
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sulfatide
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udp-galactose:ceramide
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galactosylceramide
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galactocerebroside
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galcer
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2.4.1.45
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myelin-specific
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3'-phosphohydrolase
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3'-phosphodiesterase
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myelin-related
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sulfoglycolipids
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udp-glucose:ceramide
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galactosphingolipids
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paranodal
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medicine
- 2.4.1.47
- myelin
- oligodendrocyte
- sulfatide
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udp-galactose:ceramide
- galactosylceramide
- galactocerebroside
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galcer
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2.4.1.45
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myelin-specific
-
3'-phosphohydrolase
- 3'-phosphodiesterase
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myelin-related
-
sulfoglycolipids
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udp-glucose:ceramide
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galactosphingolipids
-
paranodal
- medicine
Reaction
Synonyms
ceramide galactosyltransferase, cerebroside synthase, CGalT, CGT, EC 2.4.1.45, galactosyltransferase, uridine diphosphogalactose-2-hydroxyacylsphingosine, galactosyltransferase, uridine diphosphogalactose-acylsphingosine, GALT, UDP galactose-N-acylsphingosine galactosyltransferase, UDPgalactose-2-hydroxyacylsphingosine galactosyltransferase, UDPgalactose:2-2-hydroxyacylsphingosine galactosyltransferase, UDPgalactose:ceramide galactosyltransferase, UGT8, uridine diphosphogalactose-2-hydroxyacylsphingosine galactosyltransferase, uridine diphosphogalactose-acylsphingosine galactosyltransferase
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Localization
Localization on EC 2.4.1.47 - N-acylsphingosine galactosyltransferase
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integrated into ER membrane, enzymatically active part of CGT may be oriented toward the lumen of the ER
additional information
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activity can also be found to a minor degree in mitochondrial fraction
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translation product with N-terminal 20 amino acids signal sequence, C-terminal 23 amino acids transmembrane domain and KKVK endoplasmic reticulum retention signal
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with transmembrane helical domain, hydrophobic sequence of 20 amino acids in the C-terminal domain
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smooth endoplasmic reticulum, with C-terminal endoplasmic reticulum membrane retention signal, C-terminal 20 residue transmembrane domain as anchor of enzyme in the membrane of the ER
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smooth endoplasmic reticulum, with C-terminal endoplasmic reticulum membrane retention signal, C-terminal 20 residue transmembrane domain as anchor of enzyme in the membrane of the ER
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