Any feedback?
Please rate this page
(ecexplorer.php)
(0/150)

BRENDA support

EC Explorer

EC 2.4.1.47 Details
EC number
2.4.1.47
Accepted name
N-acylsphingosine galactosyltransferase
Reaction
UDP-α-D-galactose + a ceramide = UDP + a β-D-galactosylceramide
Other name(s)
UGT8 (gene name), CGT (gene name), UDP galactose-N-acylsphingosine galactosyltransferase, uridine diphosphogalactose-acylsphingosine galactosyltransferase, UDP-galactose:N-acylsphingosine D-galactosyltransferase, UDP-α-D-galactose:N-acylsphingosine D-galactosyltransferase, 2-hydroxyacylsphingosine 1-β-galactosyltransferase
Systematic name
UDP-α-D-galactose:N-acylsphingosine β-D-galactosyltransferase (configuration-inverting)
CAS registry number
37277-56-8
Comment
This membrane-bound, endoplasmic reticulum-located enzyme catalyses the last step in the synthesis of galactocerebrosides, which are abundant sphingolipids of the myelin membrane of the central nervous system and peripheral nervous system. It has a strong preference for ceramides that contain hydroxylated fatty acids.
History
created 1972
EC Tree
2.4.1.3 created 1961, deleted 1972
2.4.1.6 created 1961, deleted 1972
2.4.1.42 created 1972, deleted 1984
2.4.1.51 created 1972, deleted 1984
2.4.1.55 created 1972, deleted 1982
2.4.1.59 created 1972, deleted 1984
2.4.1.61 created 1972, deleted 1984
2.4.1.72 created 1972, deleted 1976
2.4.1.75 created 1976, deleted 2005
2.4.1.76 created 1976, deleted 1984
2.4.1.77 created 1976, deleted 1984
2.4.1.84 created 1976, deleted 1984
2.4.1.89 created 1976, deleted 1984
2.4.1.93 created 1976, deleted 2004
2.4.1.98 created 1980, deleted 1984
2.4.1.107 created 1983, deleted 1984
2.4.1.108 created 1983, deleted 1984
2.4.1.124 created 1984, deleted 2002
2.4.1.151 created 1984, deleted 2002
2.4.1.169 created 1989, deleted 2003
2.4.1.200 created 1992, deleted 2004
2.4.1.204 created 1992, deleted 2003
2.4.1.233 created 2004, deleted 2005