EC Number |
Natural Substrates |
---|
2.8.3.5 | succinyl-CoA + acetoacetate |
key enzyme in ketone body metabolism |
2.8.3.5 | succinyl-CoA + acetoacetate |
liver enzyme: produces a substrate circle between acetoacetyl-CoA and acetoacetate |
2.8.3.5 | succinyl-CoA + acetoacetate |
rate determining step of ketolysis in extrahepatic tissues |
2.8.3.5 | succinyl-CoA + acetoacetate |
enzyme deficiency leads to ketoacidotic crises and persistent ketosis |
2.8.3.5 | succinyl-CoA + beta-hydroxybutyrate |
- |
2.8.3.5 | succinyl-CoA + beta-hydroxybutyrate |
essential enzyme in the metabolism of ketone bodies in higher animals |