EC Number |
BRENDA No. |
Title |
Journal |
Volume |
Pages |
Year |
Organism |
PubMed ID |
---|
1.3.8.6 | 742629 |
Disease-causing mutations affecting surface residues of mitochondrial glutaryl-CoA dehydrogenase impair stability, heteromeric complex formation and mitochondria architecture |
Hum. Mol. Genet. |
26 |
538-551 |
2017 |
Homo sapiens |
28062662 |
1.3.8.6 | 743361 |
Immunolocalization of glutaryl-CoA dehydrogenase (GCDH) in adult and embryonic rat brain and peripheral tissues |
Neuroscience |
343 |
355-363 |
2017 |
Rattus norvegicus |
27984186 |
1.3.8.6 | 743652 |
Interaction of glutaric aciduria type 1-related glutaryl-CoA dehydrogenase with mitochondrial matrix proteins |
PLoS ONE |
9 |
e87715 |
2014 |
Homo sapiens |
24498361 |
1.3.8.6 | 762752 |
Potential complementation effects of two disease-associated mutations in tetrameric glutaryl-CoA dehydrogenase is due to inter subunit stability-activity counterbalance |
Biochim. Biophys. Acta |
1868 |
140269 |
2020 |
Homo sapiens |
31491587 |
1.3.8.6 | 391419 |
Alternate substrates of human glutaryl-CoA dehydrogenase: Structure and reactivity of substrates, and identification of a novel 2-enoyl-CoA product |
Biochemistry |
41 |
1274-1284 |
2002 |
Homo sapiens |
11802727 |
1.3.8.6 | 391421 |
Analysis of the expression of murine glutaryl-CoA dehydrogenase: in vitro and in vivo studies |
Mol. Genet. Metab. |
69 |
116-122 |
2000 |
Mus musculus |
10720438 |
1.3.8.6 | 391418 |
Binding, hydration, and decarboxylation of the reaction intermediate glutaconyl-Coenzyme A by human Glutaryl-CoA dehydrogenase |
Biochemistry |
40 |
14106-14114 |
2001 |
Homo sapiens |
11705404 |
1.3.8.6 | 688179 |
Biochemistry and bioenergetics of glutaryl-CoA dehydrogenase deficiency |
J. Inherit. Metab. Dis. |
30 |
673-680 |
2007 |
Homo sapiens |
17879145 |
1.3.8.6 | 391413 |
Biochemistry of glutaric aciduria type I: activities of in vitro expressed wild-type and mutant cDNA encoding human glutaryl-CoA dehydrogenase |
J. Inherit. Metab. Dis. |
22 |
256-258 |
1999 |
Homo sapiens |
10384381 |
1.3.8.6 | 711644 |
Cerebral haemodynamics in patients with glutaryl-coenzyme A dehydrogenase deficiency |
Brain |
133 |
76-92 |
2010 |
Homo sapiens |
20032085 |