EC Number |
Natural Substrates |
---|
5.4.99.2 | (R)-2-Methyl-3-oxopropanoyl-CoA |
- |
5.4.99.2 | (R)-2-Methyl-3-oxopropanoyl-CoA |
key position in metabolism of propionic acid |
5.4.99.2 | (R)-2-methylmalonyl-CoA |
- |
5.4.99.2 | (R)-2-methylmalonyl-CoA |
MCM forms a complex with MeaB |
5.4.99.2 | (R)-methylmalonyl-CoA |
- |
5.4.99.2 | (R)-methylmalonyl-CoA |
the enzyme is involved in the 3-hydroxypropionate/4-hydroxybutyrate carbon fixation pathway |
5.4.99.2 | more |
this enzyme is deficient in methylmalonic acidemia |
5.4.99.2 | more |
acts as a cobalamin binding protein |
5.4.99.2 | Succinyl-CoA |
succinyl-CoA is isomerized to methylmalonyl-CoA before incorporation into the macrocyclic lactone of erythromycin |
5.4.99.2 | Succinyl-CoA |
production of propionate from succinate |