EC Number   |
Natural Substrates |
|---|
   3.2.1.76 | 2,5-anhydro-3-O-alpha-L-idopyranuronosyl-D-mannitol + H2O |
- |
| 3.2.1.76 | 2,5-anhydro-4-O-alpha-L-idopyranuronosyl-D-mannitol 6-sulfate + H2O |
- |
| 3.2.1.76 | 4-methylumbelliferyl alpha-L-iduronide + H2O |
- |
| 3.2.1.76 | alpha-L-iduronosyl-(1->3)-2,5-anhydro-D-talitol 4-sulfate + H2O |
- |
| 3.2.1.76 | anhydromannitol iduronide + H2O |
- |
| 3.2.1.76 | dermatan sulfate + H2O |
- |
| 3.2.1.76 | glycosaminoglycan + H2O |
- |
| 3.2.1.76 | heparan sulfate + H2O |
- |
| 3.2.1.76 | more |
cleaves alpha-L-iduronic acid from the nonreducing ends of dermatan sulfate, heparin, and heparan sulfate, deficiency in alpha-L-iduronidase causes mucopolysaccharidosis type I |
| 3.2.1.76 | more |
involved in the degradation of dermatan sulfate and heparan sulfate |
