EC Number   |
Natural Substrates |
|---|
    3.2.1.22 | D-galactosyl-D-galactosyl-D-glucosyl-N-acylsphingosine + H2O |
- |
| 3.2.1.22 | globotriaosylceramide + H2O |
- |
| 3.2.1.22 | globotriaosylceramide + H2O |
i.e. D-Galalpha(1,4)D-Galalpha(1,4)D-Glu-ceramide |
| 3.2.1.22 | guar gum + H2O |
- |
| 3.2.1.22 | locust bean gum + H2O |
- |
| 3.2.1.22 | melibiose + H2O |
- |
| 3.2.1.22 | melibiose + H2O |
42.1% of the activity with p-nitrophenyl alpha-D-galactopyranoside |
| 3.2.1.22 | more |
Fabry disease is a X-linked inborn error of glycolipid metabolism caused by deficiency of the lysosomal enzyme alpha-galactosidase A |
| 3.2.1.22 | more |
Fabry disease is a X-linked inborn error of glycolipid metabolism caused by deficiency of the lysosomal enzyme alpha-galactosidase A. This enzyme is responsible for the hydrolysis of terminal alpha-galactosidase linkages in various glycolipids |
| 3.2.1.22 | more |
raffinose induces about twice the activity than melibiose |
