EC Number   |
Natural Substrates |
|---|
    1.3.8.8 | 2,6-dimethylheptanoyl-CoA + oxidized flavin |
specific LCAD substrate |
| 1.3.8.8 | lauroyl-CoA + acceptor |
enzyme shows preference for long-chain fatty acids |
| 1.3.8.8 | more |
enzyme deficiency may ba a cause of autism, physiological alterations in case of enzyme deficiency are in TCA energy metabolism, ammonia detoxification, and synthesis of omega-3 DHA, and elevated acyl-carnitine levels, the mitochondrial enzyme is responsible for beta-oxidation of branched and unsaturated fatty acids with preference for long-chain fatty acids |
| 1.3.8.8 | more |
catalyses the initial step of mitochondrial beta-oxidation of long-chain fatty acids with a chain length of 14 to 20 carbons |
| 1.3.8.8 | palmitoyl-CoA + electron-transfer flavoprotein |
enzyme does not affect all acyl-CoA utilizing cellular processes |
