EC Number |
Natural Substrates |
---|
1.3.8.6 | glutaryl-CoA + acceptor |
- |
1.3.8.6 | glutaryl-CoA + acceptor |
involved in mitochondrial degradation of lysine, hydroxylysine, tryptophan |
1.3.8.6 | glutaryl-CoA + acceptor |
analysis of mutations causing glutaric acidemia type I |
1.3.8.6 | glutaryl-CoA + acceptor |
deficiency causes glutaric aciduria type I, study on activities in wild type and mutants |
1.3.8.6 | glutaryl-CoA + acceptor |
part of the degradative pathway of the amino acids tryptophan, lysine, and hydroxylysine, enzyme deficiency leads to glutaric aciduria type I leading to nonspecific developmental delay, hypotonia, and macrocephaly with cerebral atrophyof prenatal onset |
1.3.8.6 | glutaryl-CoA + electron transfer flavoprotein |
- |
1.3.8.6 | glutaryl-CoA + electron transfer protein |
- |
1.3.8.6 | glutaryl-CoA + electron-transfer flavoprotein |
overall reaction |
1.3.8.6 | glutaryl-CoA + FAD |
- |
1.3.8.6 | glutaryl-CoA + FAD |
via intermediate glutaconyl-CoA |