EC Number |
Natural Substrates |
---|
1.3.8.5 | (R)-2-methylbutanoyl-CoA + electron-transfer flavoprotein |
involved in the (S)-pathway of L-isoleucine oxidation, and also in the (R)-pathway of L-alloisoleucine oxidation due to interconvertion of the 3 isomers |
1.3.8.5 | (S)-2-methylbutanoyl-CoA + electron-transfer flavoprotein |
involved in the (S)-pathway of L-isoleucine oxidation, and also in the (R)-pathway of L-alloisoleucine oxidation due to interconvertion of the 3 isomers |
1.3.8.5 | 2-methylbutanoyl-CoA + electron transfer flavoprotein |
- |
1.3.8.5 | 2-methylbutanoyl-CoA + electron transfer flavoprotein |
enzyme catalyzes the third step in the oxidative metabolism of isoleucin and valine |
1.3.8.5 | more |
the enzyme plays a pivotal role in the reversal of beta-oxidation operating in anaerobic mitochondria of the parasitic nematode Ascaris suum |
1.3.8.5 | more |
the electron-transport chain of the organism and the enzyme 2-methyl-branched-chain-enoyl-CoA reductase are responsible for the NADH-dependent reduction of the branched-chain enoyl-CoAs observed in mitochondria |
1.3.8.5 | more |
expression of the enzyme is tissue-specific and developmentally regulated |
1.3.8.5 | more |
enzyme deficiency causes 2-ethylhydracrylic aciduria with excretion f 2-methylbutyrylglycine |