Refine search

Search Natural Substrates/ Products (Substrates)

Natural Substrates/ Products (Substrates): show results

Don't show organism specific information (fast!)

Search organism in taxonomic tree (slow, choose "exact" as search mode, e.g. "mammalia" for rat,human,monkey,...)

(Not possible to combine with the first option)

Refine your search

Recommended Name:

EC Number:

Organism:

Commentary (Nat. Sub.):

Natural Products:

Commentary (Nat. Pro.):

Reversibility:

Search for synonyms (with exact matching search term)

Search term:

Results 1 - 5 of 5

EC Number	Natural Substrates	Commentary (Nat. Sub.)
1.1.1.211	a long-chain (S)-3-hydroxyacyl-CoA + NAD+	-
1.1.1.211	more	trifunctional, membrane bound, beta-oxidation enzyme
1.1.1.211	more	LCHAD and mitochondrial trifunctional protein, EC 4.2.1.17, deficiency can lead to retinopathy and peripheral neuropathy
1.1.1.211	more	mutational LCHAD deficiency leads to accumulation of long-chain 3-hydroxyacylcarnitines and the severe chorioretinopathy, retinal phenotypes in enzyme deficient children, the progression of the disease can be prevented by a dietary therapy including supplementation with docosahexaenoic acid, DHA, overview
1.1.1.211	more	mutational enzyme deficiency may lead to acute fatty liver in pregnancy, a serious, often lethal hepatic disorder, overview

Results 1 - 5 of 5

Use of this online version of BRENDA is free under the CC BY 4.0 license. See terms of use for full details.

Release 2023.1 (January 2023)