3.1.2.22 additional information no effect on palmitoylation of endothelial nitric oxide synthase 3.1.2.22 additional information mutations in the enzyme protein cause the neurodegenerative disorder infantile neuronal ceroid lipofuscinosis 3.1.2.22 additional information defect in the palmitoyl-(protein) hydrolase gene causes a neurodegenerative disorder. Depalmitoylation of the still uncharacterized substrate(s) of the enzyme is critical for postnatal development or maintainance of cortical neurons 3.1.2.22 additional information the enzyme is required for the efficient lysosomal degradation of thioesters derived from S-acylated proteins 3.1.2.22 additional information enzyme deficiency causes infantile neuronal ceroid lipofuscinosis, the enzyme plays an important role in the development of the CNS 3.1.2.22 additional information enzyme deficiency causes progressive neurological and granular osmiophilic deposits, GROD, and infantile neuronal ceroid lipofuscinosis 3.1.2.22 additional information enzyme deficiency causes progressive neurological disorder infantile neuronal ceroid lipofuscinosis, INCL 3.1.2.22 additional information enzyme deficiency causes progressive neurological disorder infantile neuronal ceroid lipofuscinosis, INCL, a lysosomal storage disorder 3.1.2.22 additional information enzyme deficiency causes progressive neurological disorder infantile neuronal ceroid lipofuscinosis, INCL, molecular basis 3.1.2.22 additional information enzyme deficiency causes the infantile form of neuronal ceroid lipofuscinosis INCL, a progressive encephalopathyof children