Gene ontology ID
GO:0002169
Definition
A mitochondrial protein complex which is capable of 3-methylcrotonyl-CoA carboxylase activity. In mammals, at least, consists as a dodecamer of 6 alpha and 6 beta subunits. MCCC-alpha has a covalently bound biotin essential for the ATP-dependent carboxylation. MCCC-beta possesses carboxyltransferase activity which presumably is essential for binding to 3-methylcrotonyl-CoA
Synonyms
1. mitochondrial 3-methylcrotonyl-CoA carboxylase holoenzyme
2. mitochondrial MCCC complex
3. mitochondrial methylcrotonoyl-CoA carboxylase complex
References
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tissue/ enzyme/ localization link to BRENDA