EC Number | Cloned (Comment) | Organism |
---|---|---|
2.8.3.13 | expressed in Escherichia coli BL21(DE3) cells and HEK-293T cells | Homo sapiens |
EC Number | Protein Variants | Comment | Organism |
---|---|---|---|
2.8.3.13 | R336W | inactive | Homo sapiens |
EC Number | Localization | Comment | Organism | GeneOntology No. | Textmining |
---|---|---|---|---|---|
2.8.3.13 | mitochondrion | - |
Homo sapiens | 5739 | - |
EC Number | Molecular Weight [Da] | Molecular Weight Maximum [Da] | Comment | Organism |
---|---|---|---|---|
2.8.3.13 | 50000 | - |
x * 50000, SDS-PAGE | Homo sapiens |
EC Number | Organism | UniProt | Comment | Textmining |
---|---|---|---|---|
2.8.3.13 | Homo sapiens | Q9HAC7 | - |
- |
EC Number | Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
2.8.3.13 | 3-hydroxy-3-methylglutaryl-CoA + glutarate | highest activity | Homo sapiens | 3-hydroxy-3-methylglutarate + glutaryl-CoA | - |
? | |
2.8.3.13 | 3-hydroxy-3-methylglutaryl-CoA + succinate | - |
Homo sapiens | 3-hydroxy-3-methylglutarate + succinyl-CoA | - |
? | |
2.8.3.13 | additional information | adipate, 3-hydroxy-3-methylglutarate and itaconate are at least 10% as good as succinate in a reaction where glutaryl-CoA is used as CoA donor. Other, shorter (malonate, methylmalonate) or more polar (D- and L-2-hydroxyglutarate, malate, alpha-ketoglutarate) are poorer substrates, which react at rates between 1 and 10% of that observed with succinate | Homo sapiens | ? | - |
? |
EC Number | Subunits | Comment | Organism |
---|---|---|---|
2.8.3.13 | ? | x * 50000, SDS-PAGE | Homo sapiens |
EC Number | Synonyms | Comment | Organism |
---|---|---|---|
2.8.3.13 | C7orf10 | - |
Homo sapiens |
2.8.3.13 | C7orf10 | gene locus | Homo sapiens |