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Literature summary extracted from

  • Primassin, S.; Ter Veld, F.; Mayatepek, E.; Spiekerkoetter, U.
    Carnitine supplementation induces acylcarnitine production in tissues of very long-chain acyl-CoA dehydrogenase-deficient mice, without replenishing low free carnitine (2008), Pediatr. Res., 63, 632-637.
    View publication on PubMed

Application

EC Number Application Comment Organism
1.3.8.8 medicine VLCAD deficiency is characterized by elevated tissue levels of C14-C18 acyl-carnitines Mus musculus

Localization

EC Number Localization Comment Organism GeneOntology No. Textmining
1.3.8.9 mitochondrion
-
Mus musculus 5739
-

Organism

EC Number Organism UniProt Comment Textmining
1.3.8.8 Mus musculus
-
-
-
1.3.8.9 Mus musculus
-
-
-

Source Tissue

EC Number Source Tissue Comment Organism Textmining
1.3.8.9 blood
-
Mus musculus
-
1.3.8.9 liver
-
Mus musculus
-
1.3.8.9 skeletal muscle
-
Mus musculus
-

Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
1.3.8.8 acyl-CoA + acceptor
-
Mus musculus 2,3-dehydroacyl-CoA + reduced acceptor
-
?
1.3.8.8 palmitoyl-CoA + electron-transfer flavoprotein
-
Mus musculus (2E)-2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
?
1.3.8.9 acyl-CoA + acceptor
-
Mus musculus 2,3-dehydroacyl-CoA + reduced acceptor
-
?

Synonyms

EC Number Synonyms Comment Organism
1.3.8.8 very long-chain acyl-CoA dehydrogenase metabolizes C14-C18 acyl-carnitines Mus musculus
1.3.8.8 VLCAD
-
Mus musculus
1.3.8.9 ACADVL
-
Mus musculus
1.3.8.9 very long-chain acyl-CoA dehydrogenase
-
Mus musculus
1.3.8.9 VLCAD
-
Mus musculus