EC Number | Application | Comment | Organism |
---|---|---|---|
1.3.8.8 | medicine | VLCAD deficiency is characterized by elevated tissue levels of C14-C18 acyl-carnitines | Mus musculus |
EC Number | Localization | Comment | Organism | GeneOntology No. | Textmining |
---|---|---|---|---|---|
1.3.8.9 | mitochondrion | - |
Mus musculus | 5739 | - |
EC Number | Organism | UniProt | Comment | Textmining |
---|---|---|---|---|
1.3.8.8 | Mus musculus | - |
- |
- |
1.3.8.9 | Mus musculus | - |
- |
- |
EC Number | Source Tissue | Comment | Organism | Textmining |
---|---|---|---|---|
1.3.8.9 | blood | - |
Mus musculus | - |
1.3.8.9 | liver | - |
Mus musculus | - |
1.3.8.9 | skeletal muscle | - |
Mus musculus | - |
EC Number | Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|---|
1.3.8.8 | acyl-CoA + acceptor | - |
Mus musculus | 2,3-dehydroacyl-CoA + reduced acceptor | - |
? | |
1.3.8.8 | palmitoyl-CoA + electron-transfer flavoprotein | - |
Mus musculus | (2E)-2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein | - |
? | |
1.3.8.9 | acyl-CoA + acceptor | - |
Mus musculus | 2,3-dehydroacyl-CoA + reduced acceptor | - |
? |
EC Number | Synonyms | Comment | Organism |
---|---|---|---|
1.3.8.8 | very long-chain acyl-CoA dehydrogenase | metabolizes C14-C18 acyl-carnitines | Mus musculus |
1.3.8.8 | VLCAD | - |
Mus musculus |
1.3.8.9 | ACADVL | - |
Mus musculus |
1.3.8.9 | very long-chain acyl-CoA dehydrogenase | - |
Mus musculus |
1.3.8.9 | VLCAD | - |
Mus musculus |