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Literature summary extracted from

  • Wysocki, S.J.; Haehnel, R.
    3-Hydroxy-3-methylglutaryl-coenzyme A lyase deficiency: a review (1986), J. Inherit. Metab. Dis., 9, 225-233.
    View publication on PubMed

Application

EC Number Application Comment Organism
4.1.3.4 medicine 3-hydroxy-3-methylglutaryl-coenzyme A lyase deficiency may cause hypoglycaemia which can lead to death Homo sapiens

Natural Substrates/ Products (Substrates)

EC Number Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
4.1.3.4 (S)-3-Hydroxy-3-methylglutaryl-CoA Homo sapiens involved in ketogenesis, leucine catabolism ?
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?

Organism

EC Number Organism UniProt Comment Textmining
4.1.3.4 Homo sapiens
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Substrates and Products (Substrate)

EC Number Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
4.1.3.4 (S)-3-Hydroxy-3-methylglutaryl-CoA involved in ketogenesis, leucine catabolism Homo sapiens ?
-
?