Protein Variants | Comment | Organism |
---|---|---|
R385S | mutant leading to biochemical abnormalities and clinical symptoms in heterozygous individuals | Homo sapiens |
Localization | Comment | Organism | GeneOntology No. | Textmining |
---|---|---|---|---|
mitochondrion | - |
Homo sapiens | 5739 | - |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
ATP + 3-methylcrotonyl-CoA + HCO3- | Homo sapiens | - |
ADP + 3-methylglutaconyl-CoA + phosphate | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
- |
- |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
fibroblast | - |
Homo sapiens | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
ATP + 3-methylcrotonyl-CoA + HCO3- | - |
Homo sapiens | ADP + 3-methylglutaconyl-CoA + phosphate | - |
? |
Subunits | Comment | Organism |
---|---|---|
heteromer | alphabeta | Homo sapiens |
Synonyms | Comment | Organism |
---|---|---|
MCC | - |
Homo sapiens |