General Stability | Organism |
---|---|
ASL undergoes cold dissociation via a dimer intermediate | Homo sapiens |
Inhibitors | Comment | Organism | Structure |
---|---|---|---|
citrulline | noncompetitive vs. fumarate and arginine | Homo sapiens | |
succinate | noncompetitive vs. fumarate and arginine | Homo sapiens |
KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.2 | - |
argininosuccinate | - |
Homo sapiens | |
3 | - |
arginine | - |
Homo sapiens | |
5.3 | - |
fumarate | - |
Homo sapiens |
Localization | Comment | Organism | GeneOntology No. | Textmining |
---|---|---|---|---|
cytosol | - |
Homo sapiens | 5829 | - |
Molecular Weight [Da] | Molecular Weight Maximum [Da] | Comment | Organism |
---|---|---|---|
51600 | - |
4 * 51600, deduced from nucleotide sequence | Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
(Nomega-L-arginino)succinate | Homo sapiens | - |
fumarate + L-arginine | - |
r |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
mutations in ASL result the clinical condition argininosuccinate aciuria | - |
Purification (Comment) | Organism |
---|---|
liver ASL | Homo sapiens |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
brain | - |
Homo sapiens | - |
erythrocyte | - |
Homo sapiens | - |
heart | - |
Homo sapiens | - |
kidney | - |
Homo sapiens | - |
liver | predominant expression | Homo sapiens | - |
muscle | - |
Homo sapiens | - |
pancreas | - |
Homo sapiens | - |
skin fibroblast | - |
Homo sapiens | - |
Specific Activity Minimum [µmol/min/mg] | Specific Activity Maximum [µmol/min/mg] | Comment | Organism |
---|---|---|---|
8 | - |
synthesis of argininosuccinate | Homo sapiens |
10.3 | - |
deamination of argininosuccinate | Homo sapiens |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
(Nomega-L-arginino)succinate | - |
Homo sapiens | fumarate + L-arginine | - |
? | |
(Nomega-L-arginino)succinate | - |
Homo sapiens | fumarate + L-arginine | - |
r |
Subunits | Comment | Organism |
---|---|---|
tetramer | 4 * 51600, deduced from nucleotide sequence | Homo sapiens |
Synonyms | Comment | Organism |
---|---|---|
ASL | - |
Homo sapiens |