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Literature summary for 4.2.1.18 extracted from

  • Su, B.; Ryan, R.O.
    Metabolic biology of 3-methylglutaconic acid-uria: a new perspective (2014), J. Inherit. Metab. Dis., 37, 359-368.
    View publication on PubMedView publication on EuropePMC

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
trans-3-methylglutaconyl-CoA + H2O Homo sapiens
-
(S)-3-hydroxy-3-methylglutaryl-CoA
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens Q13825
-
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
trans-3-methylglutaconyl-CoA + H2O
-
Homo sapiens (S)-3-hydroxy-3-methylglutaryl-CoA
-
?

Synonyms

Synonyms Comment Organism
3-methylglutaconyl CoA hydratase
-
Homo sapiens
AUH
-
Homo sapiens