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Literature summary for 3.5.1.12 extracted from

  • Garganta, C.L.; Wolf, B.
    Lipoamidase activity in human serum is due to biotinidase (1990), Clin. Chim. Acta, 189, 313-326.
    View publication on PubMed

Application

Application Comment Organism
medicine plasma biotinidase activity assay for diagnosis and screen newborn infants for biotinidase deficiency, treatment of inborn metabolism errors with large doses of biotin Homo sapiens

Inhibitors

Inhibitors Comment Organism Structure
p-hydroxymercuribenzoate
-
Homo sapiens

Molecular Weight [Da]

Molecular Weight [Da] Molecular Weight Maximum [Da] Comment Organism
92000
-
gel filtration Homo sapiens

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
biotin amide + H2O Homo sapiens
-
?
-
?
epsilon-N-biotinyl-L-lysine + H2O Homo sapiens
-
?
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
human
-

Purification (Commentary)

Purification (Comment) Organism
-
Homo sapiens

Source Tissue

Source Tissue Comment Organism Textmining
blood serum, plasma, leukocytes Homo sapiens
-

Storage Stability

Storage Stability Organism
-20°C, activity decreases upon storage Homo sapiens

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
biotin amide + H2O
-
Homo sapiens ?
-
?
epsilon-N-biotinyl-L-lysine + H2O
-
Homo sapiens biotin + L-lysine
-
ir
epsilon-N-biotinyl-L-lysine + H2O
-
Homo sapiens ?
-
?

Subunits

Subunits Comment Organism
monomer 1 * 92000, SDS-PAGE Homo sapiens

pH Optimum

pH Optimum Minimum pH Optimum Maximum Comment Organism
5 8 p-(N-biotinylamino)benzoic acid as substrate Homo sapiens