Cloned (Comment) | Organism |
---|---|
expressed in Brassica rapa hairy roots | Homo sapiens |
KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.12 | - |
4-methylumbelliferyl alpha-L-iduronide | recombinant enzyme, at pH 3.5 and 37°C | Homo sapiens | |
0.13 | - |
4-methylumbelliferyl alpha-L-iduronide | Aldurazyme, at pH 3.5 and 37°C | Homo sapiens |
Localization | Comment | Organism | GeneOntology No. | Textmining |
---|---|---|---|---|
lysosome | - |
Homo sapiens | 5764 | - |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | P35475 | - |
- |
Posttranslational Modification | Comment | Organism |
---|---|---|
glycoprotein | the enzyme has 6 N-glycosylation sites | Homo sapiens |
Purification (Comment) | Organism |
---|---|
Eshmuno S column chromatography and Toyopearl phenyl 650 M column chromatography | Homo sapiens |
Source Tissue | Comment | Organism | Textmining |
---|
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
4-methylumbelliferyl alpha-L-iduronide + H2O | - |
Homo sapiens | 4-methylumbelliferone + alpha-L-iduronic acid | - |
? |
Subunits | Comment | Organism |
---|---|---|
? | x * 71000, SDS-PAGE | Homo sapiens |
Synonyms | Comment | Organism |
---|---|---|
Aldurazyme | commercial preparation | Homo sapiens |
alpha-L-iduronidase | - |
Homo sapiens |
IDUA | - |
Homo sapiens |
rIDUA_RLT | recombinant enzyme | Homo sapiens |
Turnover Number Minimum [1/s] | Turnover Number Maximum [1/s] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
9.4 | - |
4-methylumbelliferyl alpha-L-iduronide | Aldurazyme, at pH 3.5 and 37°C | Homo sapiens | |
11.8 | - |
4-methylumbelliferyl alpha-L-iduronide | recombinant enzyme, at pH 3.5 and 37°C | Homo sapiens |