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Literature summary for 3.2.1.76 extracted from

  • Wang, D.; Worsham, D.N.; Pan, D.
    Co-expression of MGMT(P140K) and alpha-L-iduronidase in primary hepatocytes from mucopolysaccharidosis type I mice enables efficient selection with metabolic correction (2008), J. Gene Med., 10, 249-259.
    View publication on PubMedView publication on EuropePMC

Organism

Organism UniProt Comment Textmining
Mus musculus
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-
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Source Tissue

Source Tissue Comment Organism Textmining
AML-12 cell
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Mus musculus
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hepatocyte
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Mus musculus
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Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
4-methylumbelliferyl-alpha-L-iduronide + H2O
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Mus musculus 4-methylumbelliferone + alpha-L-iduronic acid
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?

Synonyms

Synonyms Comment Organism
alpha-L-iduronidase
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Mus musculus
IDUA
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Mus musculus