Application | Comment | Organism |
---|---|---|
medicine | enzyme deficiency in globoid cell leucodystrophy or Krabbe disease | Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
D-galactosyl-N-acylsphingosine + H2O | Homo sapiens | - |
? | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
- |
- |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
skin fibroblast | in culture | Homo sapiens | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
D-galactosyl-N-acylsphingosine + H2O | - |
Homo sapiens | D-galactose + N-acylsphingosine | - |
? | |
D-galactosyl-N-acylsphingosine + H2O | - |
Homo sapiens | ? | - |
? | |
galactocerebroside + H2O | - |
Homo sapiens | D-galactose + N-acylceramide | - |
? |
Synonyms | Comment | Organism |
---|---|---|
GM1 ganglioside beta-galactosidase | similar enzyme, hydrolyzes galactosylceramide in presence of sodium cholate | Homo sapiens |