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Literature summary for 3.2.1.46 extracted from

  • Kobayashi, T.; Shinnoh, N.; Kuroiwa, Y.
    Metabolism of galactosylceramide in the twitcher mouse, an animal model of human globoid cell leukodystrophy (1986), Biochim. Biophys. Acta, 879, 215-220.
    View publication on PubMed

Activating Compound

Activating Compound Comment Organism Structure
taurocholate
-
Mus musculus
taurocholate
-
Homo sapiens

Application

Application Comment Organism
medicine twitcher mouse, a model for globoid cell leucodystrophy Mus musculus
medicine enzyme deficiency in globoid cell leucodystrophy or Krabbe disease Homo sapiens

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
D-galactosyl-N-acylsphingosine + H2O Mus musculus
-
?
-
?
D-galactosyl-N-acylsphingosine + H2O Homo sapiens
-
?
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-
Mus musculus
-
twitcher mouse
-

Purification (Commentary)

Purification (Comment) Organism
partially Mus musculus

Source Tissue

Source Tissue Comment Organism Textmining
liver
-
Mus musculus
-
liver
-
Homo sapiens
-
placenta
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
D-galactosyl-N-acylsphingosine + H2O
-
Mus musculus D-galactose + N-acylsphingosine
-
?
D-galactosyl-N-acylsphingosine + H2O
-
Homo sapiens D-galactose + N-acylsphingosine
-
?
D-galactosyl-N-acylsphingosine + H2O
-
Mus musculus ?
-
?
D-galactosyl-N-acylsphingosine + H2O
-
Homo sapiens ?
-
?
galactocerebroside + H2O
-
Mus musculus D-galactose + N-acylceramide
-
?
galactocerebroside + H2O
-
Homo sapiens D-galactose + N-acylceramide
-
?