Application | Comment | Organism |
---|---|---|
medicine | treatment of Pompe Disease | Cricetulus griseus |
Protein Variants | Comment | Organism |
---|---|---|
additional information | HP-GAA, carbohydraded engineered form, highest relative affinity to the soluble cation independent mannose-6-phosphate receptor | Cricetulus griseus |
Localization | Comment | Organism | GeneOntology No. | Textmining |
---|---|---|---|---|
lysosome | - |
Cricetulus griseus | 5764 | - |
Molecular Weight [Da] | Molecular Weight Maximum [Da] | Comment | Organism |
---|---|---|---|
110000 | - |
SDS-PAGE | Cricetulus griseus |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Cricetulus griseus | - |
- |
- |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
CHO cell | - |
Cricetulus griseus | - |
Specific Activity Minimum [µmol/min/mg] | Specific Activity Maximum [µmol/min/mg] | Comment | Organism |
---|---|---|---|
4.2 | - |
tgGAA | Cricetulus griseus |
4.3 | - |
isoenzyme CHO-GAA | Cricetulus griseus |
4.5 | - |
isoenzyme HP-GAA | Cricetulus griseus |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
4-methylumbelliferyl-alpha-D-glucoside | pH 4.0, 60 min, 37°C | Cricetulus griseus | 4-methylumbelliferone + alpha-D-glucose | - |
? | |
4-nitrophenyl D-alpha-glucopyranoside + H2O | pH 4.3 | Cricetulus griseus | 4-nitrophenol + D-glucose | - |
? |
Synonyms | Comment | Organism |
---|---|---|
acid alpha-glucosidase | - |
Cricetulus griseus |
CHO-GAA | - |
Cricetulus griseus |
GAA | - |
Cricetulus griseus |
HP-GAA | - |
Cricetulus griseus |
rhGAA | - |
Cricetulus griseus |
tgGAA | - |
Cricetulus griseus |
Temperature Optimum [°C] | Temperature Optimum Maximum [°C] | Comment | Organism |
---|---|---|---|
37 | - |
pH 4.0-4.3, 60 min | Cricetulus griseus |
pH Minimum | pH Maximum | Comment | Organism |
---|---|---|---|
4 | 4.3 | 37°C, 60 min | Cricetulus griseus |
Organism | Comment | pI Value Maximum | pI Value |
---|---|---|---|
Cricetulus griseus | CHO-GAA, IEF-Gel | 4.6 | 4 |
Cricetulus griseus | tgGAA, IEF-Gel | 4.6 | 4.2 |
Cricetulus griseus | HP-GAA, IEF-Gel | 4.9 | 4.6 |