Literature summary for 3.10.1.1 extracted from

King, B.; Savas, P.; Fuller, M.; Hopwood, J.; Hemsley, K.
Validation of a heparan sulfate-derived disaccharide as a marker of accumulation in murine mucopolysaccharidosis type IIIA (2006), Mol. Genet. Metab., 87, 107-112.

Application

Application	Comment	Organism
medicine	the relative quantification of hexosamine-N-sulfate[alpha-1,4]hexuronic acid should prove to be a useful indicator of the effectiveness of enzyme replacement therapy within the mucopolysaccharidosis type IIIA mouse central nervous system	Mus musculus

Organism	UniProt	Comment	Textmining
Mus musculus	-	-	-

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Release 2023.1 (January 2023)