Application | Comment | Organism |
---|---|---|
medicine | deficiency in Maroteaux-Lamy syndrome, mucopolysaccharidosis type IV | Homo sapiens |
KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.06 | - |
4-Methylumbelliferyl sulfate | pH 3.5 | Homo sapiens |
Localization | Comment | Organism | GeneOntology No. | Textmining |
---|---|---|---|---|
lysosome | - |
Homo sapiens | 5764 | - |
Molecular Weight [Da] | Molecular Weight Maximum [Da] | Comment | Organism |
---|---|---|---|
13000 | - |
1 * 57000, composed of 2 peptides 1 * 43000, 1 * 13000 | Homo sapiens |
43000 | - |
1 * 57000, composed of 2 peptides 1 * 43000, 1 * 13000 | Homo sapiens |
57000 | - |
SDS-PAGE | Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
N-acetyl-D-galactosamine 4-sulfate units + H2O | Homo sapiens | acts also on N-acetylglucosamine 4-sulfate | N-acetyl-D-galactosamine units + sulfate | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
- |
- |
Purification (Comment) | Organism |
---|---|
- |
Homo sapiens |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
liver | - |
Homo sapiens | - |
Specific Activity Minimum [µmol/min/mg] | Specific Activity Maximum [µmol/min/mg] | Comment | Organism |
---|---|---|---|
0.282 | - |
- |
Homo sapiens |
93.3 | - |
nitrocatechol sulfate | Homo sapiens |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
4-methylumbelliferyl sulfate + H2O | - |
Homo sapiens | 4-methylumbelliferone + sulfate | - |
? | |
N-acetygalactosamine 4-sulfate-(1-4)-beta-glucuronic acid-(1-3)-beta-N-acetylgalactosaminitol 4-sulfate + H2O | oligosaccharides | Homo sapiens | N-acetygalactosamine-(1-4)-beta glucuronic acid-(1-3)-beta N-acetylgalactosaminitol 4-sulfate + sulfate | - |
? | |
N-acetyl-D-galactosamine 4-sulfate units + H2O | acts also on N-acetylglucosamine 4-sulfate | Homo sapiens | N-acetyl-D-galactosamine units + sulfate | - |
? |
Subunits | Comment | Organism |
---|---|---|
monomer | 1 * 57000, composed of 2 peptides 1 * 43000, 1 * 13000 | Homo sapiens |
pH Optimum Minimum | pH Optimum Maximum | Comment | Organism |
---|---|---|---|
3.8 | - |
oligosaccharide substrate, formate buffer | Homo sapiens |
4.4 | - |
oligosaccharide substrate, acetate buffer or dimethylglutarate buffer | Homo sapiens |
5.5 | - |
4-methylumbelliferyl sulfate | Homo sapiens |