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Literature summary for 3.1.4.12 extracted from

  • Rousson, R.; Bonnet, J.; Louisot, P.; Vanier, M.T.
    Presence of immunoreactive material in Niemann-Pick type A placenta using anti-sphingomyelinase rabbit gammaglobulins (1987), Biochim. Biophys. Acta, 924, 502-508.
    View publication on PubMed

KM Value [mM]

KM Value [mM] KM Value Maximum [mM] Substrate Comment Organism Structure
additional information
-
sphingomyelin comparison of values from enzymes of normal and mutated tissues Homo sapiens
additional information
-
sphingomyelin influence of detergents Homo sapiens

Molecular Weight [Da]

Molecular Weight [Da] Molecular Weight Maximum [Da] Comment Organism
57000
-
1 * 70000 + 1 * 57000, SDS-PAGE + western blotting analysis Homo sapiens
70000
-
1 * 70000 + 1 * 57000, SDS-PAGE + western blotting analysis Homo sapiens

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
sphingomyelin + H2O Homo sapiens
-
?
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Purification (Commentary)

Purification (Comment) Organism
-
Homo sapiens

Source Tissue

Source Tissue Comment Organism Textmining
placenta
-
Homo sapiens
-

Specific Activity [micromol/min/mg]

Specific Activity Minimum [µmol/min/mg] Specific Activity Maximum [µmol/min/mg] Comment Organism
additional information
-
different assay conditions, substrates etc. Homo sapiens

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
bis(4-methylumbelliferyl)-phosphate + H2O
-
Homo sapiens ?
-
?
sphingomyelin + H2O
-
Homo sapiens ?
-
?

Subunits

Subunits Comment Organism
dimer 1 * 70000 + 1 * 57000, SDS-PAGE + western blotting analysis Homo sapiens

Temperature Stability [°C]

Temperature Stability Minimum [°C] Temperature Stability Maximum [°C] Comment Organism
56
-
90 min, 50% activity, influence of detergens Homo sapiens

pH Optimum

pH Optimum Minimum pH Optimum Maximum Comment Organism
5
-
-
Homo sapiens