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Literature summary for 3.1.3.9 extracted from

  • Lee, Y.M.; Kim, G.Y.; Pan, C.J.; Mansfield, B.C.; Chou, J.Y.
    Minimal hepatic glucose-6-phosphatase-alpha activity required to sustain survival and prevent hepatocellular adenoma formation in murine glycogen storage disease type Ia (2015), Mol. Genet. Metab. Rep., 3, 28-32 .
    View publication on PubMedView publication on EuropePMC

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
D-glucose 6-phosphate + H2O Mus musculus
-
D-glucose + phosphate
-
?

Organism

Organism UniProt Comment Textmining
Mus musculus
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
liver
-
Mus musculus
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
D-glucose 6-phosphate + H2O
-
Mus musculus D-glucose + phosphate
-
?

Synonyms

Synonyms Comment Organism
G6Pase-alpha
-
Mus musculus
G6PC
-
Mus musculus
glucose-6-phosphatase-alpha
-
Mus musculus

General Information

General Information Comment Organism
malfunction glycogen storage disease type Ia characterized by impaired glucose homeostasis and chronic risk of hepatocellular adenoma, is caused by a deficiency in glucose-6-phosphatase-alpha activity Mus musculus