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Literature summary for 2.7.1.40 extracted from

  • Titapiwatanakun, R.; Hoyer, J.D.; Crain, K.; Arndt, C.A.
    Relative red blood cell enzyme levels as a clue to the diagnosis of pyruvate kinase deficiency (2008), Pediatr. Blood Cancer, 51, 819-821.
    View publication on PubMed

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
ADP + phosphoenolpyruvate Homo sapiens
-
ATP + pyruvate
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
erythrocyte
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
ADP + phosphoenolpyruvate
-
Homo sapiens ATP + pyruvate
-
?

Synonyms

Synonyms Comment Organism
phosphoenolpyruvate kinase
-
Homo sapiens

Cofactor

Cofactor Comment Organism Structure
ADP
-
Homo sapiens

Expression

Organism Comment Expression
Homo sapiens two patients with transfusion-dependent anemia reveal red blood cell pyruvate kinase to be 33% and 41% of the mean normal value down