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Literature summary for 1.3.8.9 extracted from

  • Primassin, S.; Ter Veld, F.; Mayatepek, E.; Spiekerkoetter, U.
    Carnitine supplementation induces acylcarnitine production in tissues of very long-chain acyl-CoA dehydrogenase-deficient mice, without replenishing low free carnitine (2008), Pediatr. Res., 63, 632-637.
    View publication on PubMed

Localization

Localization Comment Organism GeneOntology No. Textmining
mitochondrion
-
Mus musculus 5739
-

Organism

Organism UniProt Comment Textmining
Mus musculus
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
blood
-
Mus musculus
-
liver
-
Mus musculus
-
skeletal muscle
-
Mus musculus
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
acyl-CoA + acceptor
-
Mus musculus 2,3-dehydroacyl-CoA + reduced acceptor
-
?

Synonyms

Synonyms Comment Organism
ACADVL
-
Mus musculus
very long-chain acyl-CoA dehydrogenase
-
Mus musculus
VLCAD
-
Mus musculus