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Literature summary for 1.2.1.104 extracted from

  • Sidhu, S.; Gangasani, A.; Korotchkina, L.G.; Suzuki, G.; Fallavollita, J.A.; Canty, J.M.; Patel, M.S.
    Tissue-specific pyruvate dehydrogenase complex deficiency causes cardiac hypertrophy and sudden death of weaned male mice (2008), Am. J. Physiol. Heart Circ. Physiol., 295, H946-H952.
    View publication on PubMedView publication on EuropePMC

Activating Compound

Activating Compound Comment Organism Structure
pyruvate dehydrogenase phosphatase PDC is dephosphorylated and to completely activated with pyruvate dehydrogenase phosphatase Mus musculus

Organism

Organism UniProt Comment Textmining
Mus musculus
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
heart
-
Mus musculus
-
skeletal muscle
-
Mus musculus
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
pyruvate + CoA + NAD+
-
Mus musculus acetyl-CoA + CO2 + NADH
-
?

Synonyms

Synonyms Comment Organism
PDC
-
Mus musculus
pyruvate dehydrogenase complex multienzyme complex composed of three catalytic components (pyruvate dehydrogenase, dihydrolipoamide acetyltransferase, and dihydrolipoamide dehydrogenase), one binding protein (dihydrolipoamide dehydrogenase-binding protein), and two regulatory enzymes (a family of pyruvate dehydrogenase kinases and a family of pyruvate dehydrogenase phosphatases) Mus musculus

Cofactor

Cofactor Comment Organism Structure
NAD+
-
Mus musculus