Molecular Weight [Da] | Molecular Weight Maximum [Da] | Comment | Organism |
---|---|---|---|
50000 | - |
4 * 50000 | Caenorhabditis elegans |
50000 | - |
4 * 50000 | Legionella pneumophila |
50000 | - |
4 * 50000 | Homo sapiens |
50000 | - |
4 * 50000 | Chromobacterium violaceum |
50000 | - |
4 * 50000 | Rattus norvegicus |
50000 | - |
4 * 50000 | Colwellia psychrerythraea |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
L-phenylalanine + tetrahydrobiopterin + O2 | Caenorhabditis elegans | - |
L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? | |
L-phenylalanine + tetrahydrobiopterin + O2 | Legionella pneumophila | - |
L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? | |
L-phenylalanine + tetrahydrobiopterin + O2 | Homo sapiens | - |
L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? | |
L-phenylalanine + tetrahydrobiopterin + O2 | Chromobacterium violaceum | - |
L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? | |
L-phenylalanine + tetrahydrobiopterin + O2 | Rattus norvegicus | - |
L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? | |
L-phenylalanine + tetrahydrobiopterin + O2 | Colwellia psychrerythraea | - |
L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? | |
L-phenylalanine + tetrahydrobiopterin + O2 | Legionella pneumophila 130b | - |
L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Caenorhabditis elegans | - |
- |
- |
Chromobacterium violaceum | P30967 | - |
- |
Colwellia psychrerythraea | Q47XN7 | - |
- |
Homo sapiens | P00439 | - |
- |
Legionella pneumophila | - |
- |
- |
Legionella pneumophila 130b | - |
- |
- |
Rattus norvegicus | P04176 | - |
- |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
L-phenylalanine + tetrahydrobiopterin + O2 | - |
Caenorhabditis elegans | L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? | |
L-phenylalanine + tetrahydrobiopterin + O2 | - |
Legionella pneumophila | L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? | |
L-phenylalanine + tetrahydrobiopterin + O2 | - |
Homo sapiens | L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? | |
L-phenylalanine + tetrahydrobiopterin + O2 | - |
Chromobacterium violaceum | L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? | |
L-phenylalanine + tetrahydrobiopterin + O2 | - |
Rattus norvegicus | L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? | |
L-phenylalanine + tetrahydrobiopterin + O2 | - |
Colwellia psychrerythraea | L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? | |
L-phenylalanine + tetrahydrobiopterin + O2 | - |
Legionella pneumophila 130b | L-tyrosine + 4a-hydroxytetrahydrobiopterin | - |
? |
Subunits | Comment | Organism |
---|---|---|
homodimer | 4 * 50000 | Caenorhabditis elegans |
homodimer | 4 * 50000 | Legionella pneumophila |
homodimer | 4 * 50000 | Homo sapiens |
homodimer | 4 * 50000 | Chromobacterium violaceum |
homodimer | 4 * 50000 | Rattus norvegicus |
homodimer | 4 * 50000 | Colwellia psychrerythraea |
Synonyms | Comment | Organism |
---|---|---|
PAH | - |
Caenorhabditis elegans |
PAH | - |
Legionella pneumophila |
PAH | - |
Homo sapiens |
PAH | - |
Chromobacterium violaceum |
PAH | - |
Rattus norvegicus |
PAH | - |
Colwellia psychrerythraea |
phenylalanine hydroxylase | - |
Caenorhabditis elegans |
phenylalanine hydroxylase | - |
Legionella pneumophila |
phenylalanine hydroxylase | - |
Homo sapiens |
phenylalanine hydroxylase | - |
Chromobacterium violaceum |
phenylalanine hydroxylase | - |
Rattus norvegicus |
phenylalanine hydroxylase | - |
Colwellia psychrerythraea |
General Information | Comment | Organism |
---|---|---|
malfunction | dysfunctional phenylalanine hydroxylase leads to phenylketonuria | Legionella pneumophila |
malfunction | dysfunctional phenylalanine hydroxylase leads to phenylketonuria | Homo sapiens |