Reference on EC 3.5.1.6 - beta-ureidopropionase
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Tamaki, N.; Mizutani, N.; Kikugawa, M.; Fujimoto, S.; Mizota, C.
Purification and properties of beta-ureidopropionase from the rat liver
Eur. J. Biochem.
169
21-26
1987
Rattus rattus
Matthews, M.M.; Traut, T.W.
Regulation of N-carbamoyl-beta-alanine amidohydrolase, the terminal enzyme in pyrimidine catabolism, by ligand-induced change in polymerization
J. Biol. Chem.
262
7232-7237
1987
Clostridium uracilicum, Euglena gracilis, Homo sapiens, Mus musculus, Rattus rattus, Clostridium uracilicum M5-2
Traut, T.W.; Loechel, S.
Pyrimidine catabolism: individual characterization of the three sequential enzymes with a new assay
Biochemistry
23
2533-2539
1984
Escherichia coli, Euglena gracilis, Mus musculus, Rattus rattus
Hardiman, M.K.; Alfant, M.; Wakelin, V.P.; Tremblay, G.C.
Capacity of rat liver for pyrimidine synthesis and catabolism during fetal and neonatal development
Arch. Biochem. Biophys.
224
326-331
1983
Rattus rattus, Rattus rattus Cd
Kaspari, H.
Repression of beta-ureidopropionase by ammonia in Rhodopseudomonas capsulata
J. Gen. Microbiol.
122
95-100
1981
Clostridium uracilicum, Euglena gracilis, Rattus rattus, Rhodobacter capsulatus, Clostridium uracilicum M5-2
-
Wasternack, C.; Lippmann, G.; Reinbotte, H.
Pyrimidine-degrading enzymes purification and properties of beta-ureidopropionase of Euglena gracilis
Biochim. Biophys. Acta
570
341-351
1979
Clostridium uracilicum, Euglena gracilis, Mus musculus, Rattus rattus, Clostridium uracilicum M5-2
Campbell, L.L.
Reductive degradation of pyrimidines. V. Enzymatic conversion of N-carbamyl-beta-alanine to beta-alanine, carbon dioxide and ammonia
J. Biol. Chem.
235
2375-2379
1960
Canis lupus familiaris, Clostridium uracilicum, Oryctolagus cuniculus, Pigeon, Rattus rattus, Clostridium uracilicum M5-2
Caravaca, J.; Grisolia, S.
Enzymatic decarbamylation of carbamyl beta-alanine and carbamyl beta-aminoisobutyric acid
J. Biol. Chem.
231
357-365
1958
Canis lupus familiaris, Oryctolagus cuniculus, Pigeon, Rattus rattus
Waldmann, G.; Podschun, B.
Assay for beta-ureidopropionase by high-performance liquid chromatography
Anal. Biochem.
188
233-236
1990
Bos taurus, Clostridium uracilicum, Euglena gracilis, Mus musculus, Rattus rattus
Ogawa, J.; Shimizu, S.
beta-Ureidopropionase with N-carbamoyl-alpha-L-amino acid amidohydrolase activity from an aerobic bacterium, Pseudomonas putida IFO 12996
Eur. J. Biochem.
223
625-630
1994
Clostridium uracilicum, Comamonas sp., Euglena gracilis, Mus musculus, Pseudomonas putida, Rattus rattus
Ogawa, J.; Kaimura, T.; Yamada, H.; Shimizu, S.
Evaluation of pyrimidine- and hydantoin-degrading enzyme activities in aerobic bacteria
FEMS Microbiol. Lett.
122
55-60
1994
Agrobacterium sp., Arthrobacter sp., Bacillus sp. (in: Bacteria), Blastobacter sp., Comamonas sp., Pseudomonas putida, Comamonas sp. E222c
-
West, T.P.
Reductive catabolism of uracil and thymine by Burkholderia cepacia
Arch. Microbiol.
168
237-239
1997
Burkholderia cepacia
-
Van Kuilenburg, A.B.P.; Van Lenthe, H.; Van Gennip, A.H.
A radiochemical assay for beta-ureidopropionase using radiolabeled N-carbamyl-beta-alanine obtained via hydrolysis of [2-14C]5,6-dihydrouracil
Anal. Biochem.
272
250-253
1999
Homo sapiens, Rattus rattus
Vreken, P.; van Kuilenburg, A.B.P.; Hamajima, N.; Meinsma, R.; van Lenthe, H.; Goehlich-Ratmann, G.; Assmann, B.E.; Wevers, R.A.; van Gennip, A.H.
cDNA cloning, genomic structure and chromosomal localization of the human BUP-1 gene encoding beta-ureidopropionase
Biochim. Biophys. Acta
1447
251-257
1999
Rattus rattus, Homo sapiens (Q9UBR1), Homo sapiens
Dobritzsch, D.; Gojkovic, Z.; Andersen, B.; Piskur, J.
Crystallization and preliminary X-ray analysis of beta-alanine synthase from the yeast Saccharomyces kluyveri
Acta Crystallogr. Sect. D
59
1267-1269
2003
Lachancea kluyveri
Lundgren, S.; Gojkovic, Z.; Piskur, J.; Dobritzsch, D.
Yeast beta-alanine synthase shares a structural scaffold and origin with dizinc-dependent exopeptidases
J. Biol. Chem.
278
51851-51862
2003
Lachancea kluyveri (Q96W94), Lachancea kluyveri
Traut, T.W.
beta-Alanine synthase, an enzyme involved in catabolism of uracil and thymine
Methods Enzymol.
324
399-410
2000
Rattus norvegicus
Walsh, T.A.; Green, S.B.; Larrinua, I.M.; Schmitzer, P.R.
Characterization of plant beta-ureidopropionase and functional overexpression in Escherichia coli
Plant Physiol.
125
1001-1011
2001
Arabidopsis sp., Zea mays
Rawls, J.M.
Analysis of pyrimidine catabolism in Drosophila melanogaster using epistatic interactions with mutations of pyrimidine biosynthesis and beta-alanine metabolism
Genetics
172
1665-1674
2006
Drosophila melanogaster
West, T.P.
Pyrimidine base catabolism in Pseudomonas putida biotype B
Antonie van Leeuwenhoek
80
163-167
2001
Pseudomonas putida
Lundgren, S.; Andersen, B.; Piskur, J.; Dobritzsch, D.
Crystallization and preliminary X-ray data analysis of beta-alanine synthase from Drosophila melanogaster
Acta Crystallogr. Sect. F
63
874-877
2007
Drosophila melanogaster
Schnackerz, K.D.; Dobritzsch, D.
Amidohydrolases of the reductive pyrimidine catabolic pathway: Purification, characterization, structure, reaction mechanisms and enzyme deficiency
Biochim. Biophys. Acta
1784
431-444
2008
Arabidopsis thaliana, Bos taurus, Caenorhabditis elegans, Dictyostelium discoideum, Drosophila melanogaster, Euglena gracilis, Homo sapiens, Pseudomonas putida, Rattus norvegicus, Zea mays, Lachancea kluyveri
Lundgren, S.; Andersen, B.; Piskur, J.; Dobritzsch, D.
Crystal structures of yeast beta-alanine synthase complexes reveal the mode of substrate binding and large scale domain closure movements
J. Biol. Chem.
282
36037-36047
2007
Lachancea kluyveri (Q96W94), Lachancea kluyveri
Lundgren, S.; Lohkamp, B.; Andersen, B.; Piskur, J.; Dobritzsch, D.
The crystal structure of beta-alanine synthase from Drosophila melanogaster reveals a homooctameric helical turn-like assembly
J. Mol. Biol.
377
1544-1559
2008
Drosophila melanogaster
van Kuilenburg, A.B.; van Lenthe, H.; van Gennip, A.H.
Activity of pyrimidine degradation enzymes in normal tissues
Nucleosides Nucleotides Nucleic Acids
25
1211-1214
2006
Homo sapiens
Thomas, H.R.; Ezzeldin, H.H.; Guarcello, V.; Mattison, L.K.; Fridley, B.L.; Diasio, R.B.
Genetic regulation of beta-ureidopropionase and its possible implication in altered uracil catabolism
Pharmacogenet. Genomics
18
25-35
2008
Homo sapiens
Martinez-Gomez, A.I.; Martinez-Rodriguez, S.; Pozo-Dengra, J.; Tessaro, D.; Servi, S.; Clemente-Jimenez, J.M.; Rodriguez-Vico, F.; Las Heras-Vazquez, F.J.
Potential application of N-carbamoyl-beta-alanine amidohydrolase from Agrobacterium tumefaciens C58 for beta-amino acid production
Appl. Environ. Microbiol.
75
514-520
2009
Agrobacterium tumefaciens, Agrobacterium tumefaciens C58 / ATCC 33970
Zrenner, R.; Riegler, H.; Marquard, C.R.; Lange, P.R.; Geserick, C.; Bartosz, C.E.; Chen, C.T.; Slocum, R.D.
A functional analysis of the pyrimidine catabolic pathway in Arabidopsis
New Phytol.
183
117-132
2009
Arabidopsis thaliana (Q8H183)
Kuhara, T.; Ohse, M.; Inoue, Y.; Shinka, T.
Five cases of beta-ureidopropionase deficiency detected by GC/MS analysis of urine metabolome
J. Mass Spectrom.
44
214-221
2009
Homo sapiens
Janowitz, T.; Ajonina, I.; Perbandt, M.; Woltersdorf, C.; Hertel, P.; Liebau, E.; Gigengack, U.
The 3-ureidopropionase of Caenorhabditis elegans, an enzyme involved in pyrimidine degradation
FEBS J.
277
4100-4109
2010
Caenorhabditis elegans (Q19437), Caenorhabditis elegans
Martinez-Gomez, A.I.; Andujar-Sanchez, M.; Clemente-Jimenez, J.M.; Neira, J.L.; Rodriguez-Vico, F.; Martinez-Rodriguez, S.; Las Heras-Vazquez, F.J.
N-Carbamoyl-beta-alanine amidohydrolase from Agrobacterium tumefaciens C58: a promiscuous enzyme for the production of amino acids
J. Chromatogr. B
879
3277-3282
2011
Agrobacterium tumefaciens, Agrobacterium tumefaciens C58 / ATCC 33970
Van Kuilenburg, A.; Dobritzsch, D.; Meijer, J.; Krumpel, M.; Selim, L.; Rashed, M.; Assmann, B.; Meinsma, R.; Lohkamp, B.; Ito, T.; Abeling, N.; Saito, K.; Eto, K.; Smitka, M.; Engvall, M.; Zhang, C.; Xu, W.; Zoetekouw, L.; Hennekam, R.
beta-Ureidopropionase deficiency: phenotype, genotype and protein structural consequences in 16 patients
Biochim. Biophys. Acta
1822
1096-1108
2012
Homo sapiens (Q9UBR1)
Lam, C.W.; Law, C.Y.; Leung, K.F.; Lai, C.K.; Pak-lam Chen, S.; Chan, B.; Chan, K.Y.; Yuen, Y.P.; Mak, C.M.; Yan-wo Chan, A.
NMR-based urinalysis for rapid diagnosis of beta-ureidopropionase deficiency in a patient with Dravet syndrome
Clin. Chim. Acta
440
201-204
2015
Homo sapiens (Q9UBR1), Homo sapiens
Meijer, J.; Nakajima, Y.; Zhang, C.; Meinsma, R.; Ito, T.; Van Kuilenburg, A.B.
Publishers note. Identification of a novel synonymous mutation in the human beta-ureidopropionase gene UPB1 affecting pre-mRNA splicing
Nucleosides Nucleotides Nucleic Acids
33
639-645
2014
Homo sapiens (Q9UBR1)
Fidlerova, J.; Kleiblova, P.; Kormunda, S.; Novotny, J.; Kleibl, Z.
Contribution of the beta-ureidopropionase (UPB1) gene alterations to the development of fluoropyrimidine-related toxicity
Pharmacol. Rep.
64
1234-1242
2012
Homo sapiens (Q9UBR1)
Shen, Y.; Chen, Y.; Liu, H.; Chiang, F.; Wang, Y.; Hou, L.; Lin, J.; Lin, C.; Lin, H.; Lai, H.; Jeng, S.
Expression of a gene encoding beta-ureidopropionase is critical for pollen germination in tomatoes
Physiol. Plant.
150
425-435
2014
Solanum lycopersicum, Solanum lycopersicum CL5915, Solanum lycopersicum L4783
Maurer, D.; Lohkamp, B.; Krumpel, M.; Widersten, M.; Dobritzsch, D.
Crystal structure and pH-dependent allosteric regulation of human beta-ureidopropionase, an enzyme involved in anticancer drug metabolism
Biochem. J.
475
2395-2416
2018
Homo sapiens (Q9UBR1)
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