Any feedback?
Please rate this page
(enzyme.php)
(0/150)

BRENDA support

Disease on EC 1.3.3.6 - acyl-CoA oxidase

Please use the Disease Search for a specific query.
Please wait a moment until all data is loaded. This message will disappear when all data is loaded.
DISEASE
TITLE OF PUBLICATION
LINK TO PUBMED
acyl-coa oxidase deficiency
A microglial cell model for acyl-CoA oxidase 1 deficiency.
A novel case of ACOX2 deficiency leads to recognition of a third human peroxisomal acyl-CoA oxidase.
A sensitive assay of acyl-coenzyme A oxidase by coupling with beta-oxidation multienzyme complex.
Acetyl-CoA Derived from Hepatic Peroxisomal ?-Oxidation Inhibits Autophagy and Promotes Steatosis via mTORC1 Activation.
ACOX2 deficiency in primary malignant cardiac tumors.
ACOX2 deficiency: A disorder of bile acid synthesis with transaminase elevation, liver fibrosis, ataxia, and cognitive impairment.
ACOX2 deficiency: An inborn error of bile acid synthesis identified in an adolescent with persistent hypertransaminasemia.
Adult peroxisomal acyl-coenzyme A oxidase deficiency with cerebellar and brainstem atrophy.
Clinical, biochemical, and mutational spectrum of peroxisomal acyl-coenzyme A oxidase deficiency.
Deep mining of oxysterols and cholestenoic acids in human plasma and cerebrospinal fluid: Quantification using isotope dilution mass spectrometry.
Distinction between peroxisomal bifunctional enzyme and acyl-CoA oxidase deficiencies.
Effects of hematopoietic stem cell transplantation on acyl-CoA oxidase deficiency: a sibling comparison study.
Epilepsy in peroxisomal diseases.
First prenatal diagnosis of acyl-CoA oxidase deficiency.
Genetic diseases caused by peroxisomal dysfunction. New findings in clinical and biochemical studies.
Hepatic peroxisomal ?-oxidation suppresses lipophagy via RPTOR acetylation and MTOR activation.
Hyperpipecolic acidaemia: a diagnostic tool for peroxisomal disorders.
Incidence of peroxisomal disorders in Japan.
Large deletion of the peroxisomal acyl-CoA oxidase gene in pseudoneonatal adrenoleukodystrophy.
Neonatal seizures and retardation in a girl with biochemical features of X-linked adrenoleukodystrophy: a possible new peroxisomal disease entity.
Novel ACOX1 mutations in two siblings with peroxisomal acyl-CoA oxidase deficiency.
Novel subtype of peroxisomal acyl-CoA oxidase deficiency and bifunctional enzyme deficiency with detectable enzyme protein: identification by means of complementation analysis.
Peroxisomal acyl CoA oxidase deficiency.
Peroxisomal acyl-CoA-oxidase deficiency: two new cases.
Peroxisomal beta-oxidation of polyunsaturated long chain fatty acids in human fibroblasts. The polyunsaturated and the saturated long chain fatty acids are retroconverted by the same acyl-CoA oxidase.
Peroxisomal disorders in neurology.
Phytanic acid alpha-oxidation and complementation analysis of classical Refsum and peroxisomal disorders.
Pitfall in metabolic screening in a patient with fatal peroxisomal beta-oxidation defect.
Prenatal and perinatal diagnosis of peroxisomal disorders.
Pristanic acid does not accumulate in peroxisomal acyl-CoA oxidase deficiency: evidence for a distinct peroxisomal pristanyl-CoA oxidase.
Separate peroxisomal oxidases for fatty acyl-CoAs and trihydroxycoprostanoyl-CoA in human liver.
Straight-chain acyl-CoA oxidase deficiency presenting with dysmorphia, neurodevelopmental autistic-type regression and a selective pattern of leukodystrophy.
The inflammatory response in acyl-CoA oxidase 1 deficiency (pseudoneonatal adrenoleukodystrophy).
Very large peroxisomes in distinct peroxisomal disorders (rhizomelic chondrodysplasia punctata and acyl-CoA oxidase deficiency): novel data.
[Peroxisomal acyl-CoA oxidase deficiency]
Adrenoleukodystrophy
Clinical consequences of defects in peroxisomal beta-oxidation.
Identification of the peroxisomal beta-oxidation enzymes involved in the biosynthesis of docosahexaenoic acid.
Identification of the peroxisomal beta-oxidation enzymes involved in the degradation of long-chain dicarboxylic acids.
Immunochemical and biochemical studies of fatty acid oxidation in fibroblasts of Zellweger and X-linked adrenoleukodystrophy patients.
Large deletion of the peroxisomal acyl-CoA oxidase gene in pseudoneonatal adrenoleukodystrophy.
Peroxisomal beta-oxidation enzyme proteins in adrenoleukodystrophy: distinction between X-linked adrenoleukodystrophy and neonatal adrenoleukodystrophy.
Peroxisomal beta-oxidation of polyunsaturated long chain fatty acids in human fibroblasts. The polyunsaturated and the saturated long chain fatty acids are retroconverted by the same acyl-CoA oxidase.
Peroxisomal disorders in neurology.
Peroxisomal very long chain fatty acid beta-oxidation activity is determined by the level of adrenodeukodystrophy protein (ALDP) expression.
Prenatal and perinatal diagnosis of peroxisomal disorders.
Targeted disruption of the peroxisomal fatty acyl-CoA oxidase gene: generation of a mouse model of pseudoneonatal adrenoleukodystrophy.
The inflammatory response in acyl-CoA oxidase 1 deficiency (pseudoneonatal adrenoleukodystrophy).
alpha-methylacyl-coa racemase deficiency
Clinical consequences of defects in peroxisomal beta-oxidation.
Reinvestigation of peroxisomal 3-ketoacyl-CoA thiolase deficiency: identification of the true defect at the level of d-bifunctional protein.
Astrocytoma
Enterovirus 71 induces neural cell apoptosis and autophagy through promoting ACOX1 downregulation and ROS generation.
Ataxia
ACOX2 deficiency: A disorder of bile acid synthesis with transaminase elevation, liver fibrosis, ataxia, and cognitive impairment.
Atherosclerosis
Peroxisomal Acyl-CoA Oxidase Type 1: Anti-Inflammatory and Anti-Aging Properties with a Special Emphasis on Studies with LPS and Argan Oil as a Model Transposable to Aging.
Breast Neoplasms
Expression of an estrogen-regulated variant transcript of the peroxisomal branched chain fatty acid oxidase ACOX2 in breast carcinomas.
Race-associated biological differences among luminal A and basal-like breast cancers in the Carolina Breast Cancer Study.
Carcinogenesis
ACOX1 destabilizes p73 to suppress intrinsic apoptosis pathway and regulates sensitivity to doxorubicin in lymphoma cells.
Carcinoma
Impairment of peroxisomal biogenesis in human colon carcinoma.
Carcinoma, Bronchogenic
[Polychemotherapy in inoperable bronchial carcinoma]
Carcinoma, Hepatocellular
ACOX2 is a prognostic marker and impedes the progression of hepatocellular carcinoma via PPAR? pathway.
Arachidonic and docosahexaenoic acids differentially affect the expression of fatty acyl-CoA oxidase, protein kinase C and lipid peroxidation in HepG2 cells.
Characterization of the species-specificity of peroxisome proliferators in rat and human hepatocytes.
Conjugated linoleic acid is a potent naturally occurring ligand and activator of PPARalpha.
Expression of peroxisome proliferator-activated receptor alpha, and PPARalpha regulated genes in spontaneously developed hepatocellular carcinomas in fatty acyl-CoA oxidase null mice.
Heneicosapentaenoate (21:5n-3): its incorporation into lipids and its effects on arachidonic acid and eicosanoid synthesis.
Hormonal and substrate regulation of 3-thia fatty acid metabolism in Morris 7800 C1 hepatoma cells.
Induction of peroxisomal acyl-CoA oxidase by 3-thia fatty acid, in hepatoma cells and hepatocytes in culture is modified by dexamethasone and insulin.
Localization of mRNAs encoding peroxisomal proteins in cell culture by non-radioactive in situ hybridization. Comparison of rat and human hepatoma cells and their responses to two divergent hypolipidemic drugs.
Molecular profiling of hepatocellular carcinomas developing spontaneously in acyl-CoA oxidase deficient mice: comparison with liver tumors induced in wild-type mice by a peroxisome proliferator and a genotoxic carcinogen.
Peroxisomal acyl-coenzyme A oxidase is a rate-limiting enzyme in a very-long-chain fatty acid beta-oxidation system.
Peroxisome proliferator-activated receptor alpha-responsive genes induced in the newborn but not prenatal liver of peroxisomal fatty acyl-CoA oxidase null mice.
Peroxisome proliferator-activated receptors, fatty acid oxidation, steatohepatitis and hepatocarcinogenesis.
Peroxisome proliferators and fatty acids negatively regulate liver X receptor-mediated activity and sterol biosynthesis.
Phytanic acid activates the peroxisome proliferator-activated receptor alpha (PPARalpha) in sterol carrier protein 2-/ sterol carrier protein x-deficient mice.
Progressive Endoplasmic Reticulum Stress Contributes to Hepatocarcinogenesis in Fatty Acyl-CoA Oxidase 1-Deficient Mice.
Role of peroxisome proliferator-activated receptor alpha in the expression of hepatic fatty acid oxidation-related genes in chickens.
The effect of retinoids and clofibric acid on the peroxisomal oxidation of palmitic acid and of 3 alpha,7 alpha,12 alpha-trihydroxy-5 beta-cholestanoic acid in rat and rabbit hepatocytes.
Cardiomegaly
Down-regulation of acyl-CoA oxidase gene expression and increased NF-kappaB activity in etomoxir-induced cardiac hypertrophy.
Cardiovascular Diseases
Identification of ACOX2 as a shared genetic risk factor for preeclampsia and cardiovascular disease.
Chondrodysplasia Punctata
Peroxisomal disorders in neurology.
Prenatal and perinatal diagnosis of peroxisomal disorders.
Very large peroxisomes in distinct peroxisomal disorders (rhizomelic chondrodysplasia punctata and acyl-CoA oxidase deficiency): novel data.
Chondrodysplasia Punctata, Rhizomelic
Epilepsy in peroxisomal diseases.
Hyperpipecolic acidaemia: a diagnostic tool for peroxisomal disorders.
Identification of the peroxisomal beta-oxidation enzymes involved in the biosynthesis of docosahexaenoic acid.
Identification of the peroxisomal beta-oxidation enzymes involved in the degradation of long-chain dicarboxylic acids.
Very large peroxisomes in distinct peroxisomal disorders (rhizomelic chondrodysplasia punctata and acyl-CoA oxidase deficiency): novel data.
Colitis
Taraxacum officinale extract ameliorates dextran sodium sulphate-induced colitis by regulating fatty acid degradation and microbial dysbiosis.
Dehydration
A hybrid next generation transcript sequencing-based approach to identify allelic and homeolog-specific single nucleotide polymorphisms in allotetraploid white clover.
Demyelinating Diseases
Peroxisomal acyl CoA oxidase deficiency.
The inflammatory response in acyl-CoA oxidase 1 deficiency (pseudoneonatal adrenoleukodystrophy).
Eosinophilia
Induction of hepatic peroxisome proliferation in mice by lactofen, a diphenyl ether herbicide.
Fatty Liver
Adaptations of hepatic lipid metabolism and mitochondria in dairy cows with mild fatty liver.
Chronic alcohol-induced liver injury and oxidant stress are decreased in cytochrome P4502E1 knockout mice and restored in humanized cytochrome P4502E1 knock-in mice.
Fenretinide ameliorates insulin resistance and Fatty liver in obese mice.
Inhibition of aldose reductase ameliorates diet-induced nonalcoholic steatohepatitis in mice via modulating the phosphorylation of hepatic peroxisome proliferator-activated receptor ?.
More than additive effects on liver triglyceride accumulation by combinations of steatotic and non-steatotic pesticides in HepaRG cells.
Peroxisomal and mitochondrial fatty acid beta-oxidation in mice nullizygous for both peroxisome proliferator-activated receptor alpha and peroxisomal fatty acyl-CoA oxidase. Genotype correlation with fatty liver phenotype.
Peroxisomal beta-oxidation and peroxisome proliferator-activated receptor alpha: an adaptive metabolic system.
Peroxisomal beta-oxidation and steatohepatitis.
Profiling of acyl-CoA oxidase-deficient and peroxisome proliferator Wy14,643-treated mouse liver protein by surface-enhanced laser desorption/ionization ProteinChip Biology System.
Progressive Endoplasmic Reticulum Stress Contributes to Hepatocarcinogenesis in Fatty Acyl-CoA Oxidase 1-Deficient Mice.
Steatohepatitis, spontaneous peroxisome proliferation and liver tumors in mice lacking peroxisomal fatty acyl-CoA oxidase. Implications for peroxisome proliferator-activated receptor alpha natural ligand metabolism.
Follicular Cyst
Alterations in key metabolic sensors involved in bovine cystic ovarian disease.
Genetic Diseases, Inborn
Genetic diseases caused by peroxisomal dysfunction. New findings in clinical and biochemical studies.
Prenatal and perinatal diagnosis of peroxisomal disorders.
Glioma
Lipid metabolism impairment in human gliomas: expression of peroxisomal proteins in human gliomas at different grades of malignancy.
Heart Failure
The PPARalpha activator fenofibrate slows down the progression of the left ventricular dysfunction in porcine tachycardia-induced cardiomyopathy.
Heart Neoplasms
ACOX2 deficiency in primary malignant cardiac tumors.
Combined effects of FH (E404D) and ACOX2 (R409H) cause metabolic defects in primary cardiac malignant tumor.
Hepatoblastoma
ACOX2 deficiency: An inborn error of bile acid synthesis identified in an adolescent with persistent hypertransaminasemia.
Hepatomegaly
Do peroxisome proliferating compounds pose a hepatocarcinogenic hazard to humans?
Do peroxisome proliferating compounds pose a hepatocarcinogenic hazard to humans?
Dose-response relationships of hepatic acyl-CoA oxidase and catalase activity and liver mitogenesis induced by the peroxisome proliferator ciprofibrate in C57BL/6N and BALB/c mice.
Effect of di(2-ethylhexyl)phthalate on enzyme activity levels in liver and serum of rats.
Experimental studies on pharmacology, metabolism and toxicology with tiadenol-disulfoxide. Dissociation of lipid lowering effects and the induction of peroxisomal and microsomal drug-metabolizing enzymes.
Properties of a fluorescent bezafibrate derivative (DNS-X). A new tool to study peroxisome proliferation and fatty acid beta-oxidation.
Hyperinsulinism
Effect of Saxagliptin, a Dipeptidyl Peptidase 4 Inhibitor, on Non-Alcoholic Fatty Liver Disease.
Hyperlipidemias
[Lipid-lowering effect and mechanism of Danhong Injection on hyperlipidemia rats based on lipid metabolism disorder].
Hyperoxaluria
Genetic diseases caused by peroxisomal dysfunction. New findings in clinical and biochemical studies.
Prenatal and perinatal diagnosis of peroxisomal disorders.
Hypertension
Increased expression of acyl-CoA oxidase 2 in the kidney with plasma phytanic acid and altered gut microbiota in spontaneously hypertensive rats.
Hypothyroidism
Triiodothyronine induces lipid oxidation and mitochondrial biogenesis in rat Harderian gland.
Infections
Enterovirus 71 induces neural cell apoptosis and autophagy through promoting ACOX1 downregulation and ROS generation.
Quantitative proteomics and phosphoproteomic analyses of mouse livers after tick-borne Babesia microti infection.
Insulin Resistance
(-)-Epigallocatechin gallate enhances the expression of genes related to insulin sensitivity and adipocyte differentiation in 3T3-L1 adipocytes at an early stage of differentiation.
Globular adiponectin protected ob/ob mice from diabetes and ApoE-deficient mice from atherosclerosis.
Leukemia, Myeloid, Acute
Expression and prognostic relevance of long noncoding RNAs CRNDE and AOX2P in adult acute myeloid leukemia.
Liver Cirrhosis
ACOX2 deficiency: A disorder of bile acid synthesis with transaminase elevation, liver fibrosis, ataxia, and cognitive impairment.
Liver Diseases
n-3 Polyunsaturated fatty acids for the management of alcoholic liver disease: A critical review.
TXNIP/VDUP1 attenuates steatohepatitis via autophagy and fatty acid oxidation.
Liver Diseases, Alcoholic
n-3 Polyunsaturated fatty acids for the management of alcoholic liver disease: A critical review.
Liver Neoplasms
ACOX2 is a prognostic marker and impedes the progression of hepatocellular carcinoma via PPAR? pathway.
Peroxisomal beta-oxidation and peroxisome proliferator-activated receptor alpha: an adaptive metabolic system.
SIRT5 inhibits peroxisomal ACOX1 to prevent oxidative damage and is downregulated in liver cancer.
Liver Neoplasms, Experimental
Synergistic actions of tetradecylthioacetic acid (TTA) and dexamethasone on induction of the peroxisomal beta-oxidation and on growth inhibition of Morris hepatoma cells. Both effects are counteracted by insulin.
Synergistic induction of acyl-CoA oxidase activity, an indicator of peroxisome proliferation, by arachidonic acid and retinoic acid in Morris hepatoma 7800C1 cells.
Lung Neoplasms
Screening of key genes and prediction of therapeutic agents in Arsenic-induced lung carcinoma.
Lymphoma
ACOX1 destabilizes p73 to suppress intrinsic apoptosis pathway and regulates sensitivity to doxorubicin in lymphoma cells.
Lymphoma, B-Cell
Silencing PEX26 as an unconventional mode to kill drug-resistant cancer cells and forestall drug resistance.
Lymphoma, Large B-Cell, Diffuse
Silencing PEX26 as an unconventional mode to kill drug-resistant cancer cells and forestall drug resistance.
Malnutrition
Evidence for liver energy metabolism programming in offspring subjected to intrauterine undernutrition during midgestation.
Memory Disorders
Inhibitor of cyclooxygenase-2 protects against amyloid beta peptide-evoked memory impairment in mice.
Metabolic Diseases
Specific Inhibition of Acyl-CoA Oxidase-1 by an Acetylenic Acid Improves Hepatic Lipid and Reactive Oxygen Species (ROS) Metabolism in Rats Fed a High Fat Diet.
Metabolic Syndrome
Peroxisomal Acyl-CoA Oxidase Type 1: Anti-Inflammatory and Anti-Aging Properties with a Special Emphasis on Studies with LPS and Argan Oil as a Model Transposable to Aging.
Muscle Hypotonia
Clinical consequences of defects in peroxisomal beta-oxidation.
Novel ACOX1 mutations in two siblings with peroxisomal acyl-CoA oxidase deficiency.
Neoplasm Metastasis
ACOX2 is a prognostic marker and impedes the progression of hepatocellular carcinoma via PPAR? pathway.
Neoplasms
ACOX2 is a prognostic marker and impedes the progression of hepatocellular carcinoma via PPAR? pathway.
Alisol A 24-Acetate Prevents Hepatic Steatosis and Metabolic Disorders in HepG2 Cells.
circ_0005379 inhibits the progression of oral squamous cell carcinoma by regulating the miR-17-5p/acyl-CoA oxidase 1 axis.
Combined effects of FH (E404D) and ACOX2 (R409H) cause metabolic defects in primary cardiac malignant tumor.
Expression of Lipid Metabolism-Related Proteins Differs between Invasive Lobular Carcinoma and Invasive Ductal Carcinoma.
Hydrogen peroxide generation in peroxisome proliferator-induced oncogenesis.
Lipid metabolism impairment in human gliomas: expression of peroxisomal proteins in human gliomas at different grades of malignancy.
Molecular profiling of hepatocellular carcinomas developing spontaneously in acyl-CoA oxidase deficient mice: comparison with liver tumors induced in wild-type mice by a peroxisome proliferator and a genotoxic carcinogen.
n-3 Polyunsaturated fatty acids for the management of alcoholic liver disease: A critical review.
Overexpression of peroxisome proliferator-activated receptor-alpha (PPARalpha)-regulated genes in liver in the absence of peroxisome proliferation in mice deficient in both L- and D-forms of enoyl-CoA hydratase/dehydrogenase enzymes of peroxisomal beta-oxidation system.
Rosa Mosqueta Oil Prevents Oxidative Stress and Inflammation through the Upregulation of PPAR-? and NRF2 in C57BL/6J Mice Fed a High-Fat Diet.
Steatohepatitis, spontaneous peroxisome proliferation and liver tumors in mice lacking peroxisomal fatty acyl-CoA oxidase. Implications for peroxisome proliferator-activated receptor alpha natural ligand metabolism.
Tumorigenic conversion of a non-tumorigenic rat urothelial cell line by overexpression of H2O2-generating peroxisomal fatty acyl-CoA oxidase.
TXNIP/VDUP1 attenuates steatohepatitis via autophagy and fatty acid oxidation.
Neuroblastoma
Enterovirus 71 induces neural cell apoptosis and autophagy through promoting ACOX1 downregulation and ROS generation.
Neurodegenerative Diseases
The inflammatory response in acyl-CoA oxidase 1 deficiency (pseudoneonatal adrenoleukodystrophy).
Non-alcoholic Fatty Liver Disease
Analysis of hepatic genes involved in the metabolism of fatty acids and iron in nonalcoholic fatty liver disease.
Food-drug interaction: Anabolic steroids aggravate hepatic lipotoxicity and nonalcoholic fatty liver disease induced by trans fatty acids.
Gynostemma pentaphyllum Attenuates the Progression of Nonalcoholic Fatty Liver Disease in Mice: A Biomedical Investigation Integrated with In Silico Assay.
miR-222 targets ACOX1, promotes triglyceride accumulation in hepatocytes.
n-3 Polyunsaturated fatty acids for the management of alcoholic liver disease: A critical review.
Peroxisomal ?-oxidation regulates whole body metabolism, inflammatory vigor, and pathogenesis of nonalcoholic fatty liver disease.
TXNIP/VDUP1 attenuates steatohepatitis via autophagy and fatty acid oxidation.
Obesity
Effect of maternal folic acid supplementation on hepatic one-carbon unit associated gene expressions in newborn piglets.
Hypolipidemic Activity of Peony Seed Oil Rich in ?-Linolenic, is Mediated Through Inhibition of Lipogenesis and Upregulation of Fatty Acid ?-Oxidation.
Network analysis of hepatic genes responded to high-fat diet in C57BL/6J mice: nutrigenomics data mining from recent research findings.
Ontogeny of hepatic energy metabolism genes in mice as revealed by RNA-sequencing.
Sustained activation of PPAR? by endogenous ligands increases hepatic fatty acid oxidation and prevents obesity in ob/ob mice.
Optic Atrophy
Novel mitochondrial protein interactors of immunoglobulin light chains causing heart amyloidosis.
Peroxisomal Disorders
A new peroxisomal disorder with enlarged peroxisomes and a specific deficiency of acyl-CoA oxidase (pseudo-neonatal adrenoleukodystrophy).
ACOX1 destabilizes p73 to suppress intrinsic apoptosis pathway and regulates sensitivity to doxorubicin in lymphoma cells.
Activity measurements of acyl-CoA oxidases in human liver.
Epilepsy in peroxisomal diseases.
Genetic diseases caused by peroxisomal dysfunction. New findings in clinical and biochemical studies.
Hyperpipecolic acidaemia: a diagnostic tool for peroxisomal disorders.
Peroxisomal disorders in neurology.
Phytanic acid alpha-oxidation and complementation analysis of classical Refsum and peroxisomal disorders.
Pitfall in metabolic screening in a patient with fatal peroxisomal beta-oxidation defect.
Plasma very long chain fatty acids in 3,000 peroxisome disease patients and 29,000 controls.
Prenatal and perinatal diagnosis of peroxisomal disorders.
Very large peroxisomes in distinct peroxisomal disorders (rhizomelic chondrodysplasia punctata and acyl-CoA oxidase deficiency): novel data.
Pre-Eclampsia
Identification of ACOX2 as a shared genetic risk factor for preeclampsia and cardiovascular disease.
Prostatic Neoplasms
Peroxisomal branched chain fatty acid beta-oxidation pathway is upregulated in prostate cancer.
Protein Deficiency
Prenatal and perinatal diagnosis of peroxisomal disorders.
Refsum Disease
Biosynthesis and maturation of peroxisomal beta-oxidation enzymes in fibroblasts in relation to the Zellweger syndrome and infantile Refsum disease.
Genetic diseases caused by peroxisomal dysfunction. New findings in clinical and biochemical studies.
Peroxisomal disorders in neurology.
Phytanic acid alpha-oxidation and complementation analysis of classical Refsum and peroxisomal disorders.
Prenatal and perinatal diagnosis of peroxisomal disorders.
Refsum Disease, Infantile
Infantile Refsum disease: deficiency of catalase-containing particles (peroxisomes), alkyldihydroxyacetone phosphate synthase and peroxisomal beta-oxidation enzyme proteins.
Peroxisomal disorders in neurology.
Plasma very long chain fatty acids in 3,000 peroxisome disease patients and 29,000 controls.
Prenatal and perinatal diagnosis of peroxisomal disorders.
Reperfusion Injury
Alterations of peroxisomal function in ischemia-reperfusion injury of rat kidney.
Retinoblastoma
Docosahexaenoic acid membrane content and mRNA expression of acyl-CoA oxidase and of peroxisome proliferator-activated receptor-delta are modulated in Y79 retinoblastoma cells differently by low and high doses of alpha-linolenic acid.
Sarcoma
Intralipid decreases apolipoprotein M levels and insulin sensitivity in rats.
Seizures
Clinical consequences of defects in peroxisomal beta-oxidation.
Novel ACOX1 mutations in two siblings with peroxisomal acyl-CoA oxidase deficiency.
Starvation
Acetyl-CoA Derived from Hepatic Peroxisomal ?-Oxidation Inhibits Autophagy and Promotes Steatosis via mTORC1 Activation.
Biosynthetic tailoring of existing ascaroside pheromones alters their biological function in C. elegans.
Hepatic peroxisomal ?-oxidation suppresses lipophagy via RPTOR acetylation and MTOR activation.
Peroxisomal and mitochondrial beta-oxidation in the rat kidney: distribution of fatty acyl-coenzyme A oxidase and 3-hydroxyacyl-coenzyme A dehydrogenase activities along the nephron.
Variability of ACOX1 Gene Polymorphisms across Different Horse Breeds with Regard to Selection Pressure.
Urinary Bladder Neoplasms
The prognostic significance of DAPK1 in bladder cancer.
Xanthomatosis, Cerebrotendinous
Deep mining of oxysterols and cholestenoic acids in human plasma and cerebrospinal fluid: Quantification using isotope dilution mass spectrometry.
Zellweger Syndrome
Acyl-CoA oxidase, peroxisomal thiolase and dihydroxyacetone phosphate acyltransferase: aberrant subcellular localization in Zellweger syndrome.
Biogenesis of peroxisomes in fetal liver.
Biosynthesis and maturation of peroxisomal beta-oxidation enzymes in fibroblasts in relation to the Zellweger syndrome and infantile Refsum disease.
Epilepsy in peroxisomal diseases.
Identification of pristanoyl-CoA oxidase activity in human liver and its deficiency in the Zellweger syndrome.
Identification of pristanoyl-CoA oxidase and phytanic acid decarboxylation in peroxisomes and mitochondria from human liver: implications for Zellweger syndrome.
Molecular analysis of peroxisomal beta-oxidation enzymes in infants with Zellweger syndrome and Zellweger-like syndrome: further heterogeneity of the peroxisomal disorder.
Molecular characterization of the human peroxisomal branched-chain acyl-CoA oxidase: cDNA cloning, chromosomal assignment, tissue distribution, and evidence for the absence of the protein in Zellweger syndrome.
Peroxisomal beta-oxidation enzyme proteins in adrenoleukodystrophy: distinction between X-linked adrenoleukodystrophy and neonatal adrenoleukodystrophy.
Peroxisomal beta-oxidation enzyme proteins in the Zellweger syndrome.
Peroxisomal beta-oxidation of polyunsaturated long chain fatty acids in human fibroblasts. The polyunsaturated and the saturated long chain fatty acids are retroconverted by the same acyl-CoA oxidase.
Peroxisomal disorders in neurology.
Peroxisomal very long chain fatty acid beta-oxidation activity is determined by the level of adrenodeukodystrophy protein (ALDP) expression.
Phytanic acid alpha-oxidation and complementation analysis of classical Refsum and peroxisomal disorders.
Plasma very long chain fatty acids in 3,000 peroxisome disease patients and 29,000 controls.
Prenatal and perinatal diagnosis of peroxisomal disorders.
Zellweger-like syndrome with detectable hepatic peroxisomes: a variant form of peroxisomal disorder.