6.4.1.3: propionyl-CoA carboxylase
This is an abbreviated version!
For detailed information about propionyl-CoA carboxylase, go to the full flat file.
Word Map on EC 6.4.1.3
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6.4.1.3
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propionic
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acidemia
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biotin-dependent
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carboxylases
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methylmalonyl-coa
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acidosis
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methylmalonic
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3-hydroxypropionate
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methylcitrate
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propionylation
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hyperammonemia
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holocarboxylase
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3-methylcrotonyl-coa
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acidurias
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biotin-containing
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carboxyltransferase
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biotin-deficient
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hyperglycinemia
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beta-methylcrotonyl-coa
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biotin-binding
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odd-chain
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anaplerosis
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transcarboxylase
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3-hydroxyisovaleric
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propionylcarnitine
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synthesis
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analysis
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medicine
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apocarboxylases
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biotinidase
- 6.4.1.3
- propionic
- acidemia
-
biotin-dependent
- carboxylases
- methylmalonyl-coa
- acidosis
-
methylmalonic
- 3-hydroxypropionate
-
methylcitrate
-
propionylation
-
hyperammonemia
- holocarboxylase
- 3-methylcrotonyl-coa
- acidurias
-
biotin-containing
- carboxyltransferase
-
biotin-deficient
- hyperglycinemia
- beta-methylcrotonyl-coa
-
biotin-binding
-
odd-chain
-
anaplerosis
- transcarboxylase
-
3-hydroxyisovaleric
- propionylcarnitine
- synthesis
- analysis
- medicine
- apocarboxylases
- biotinidase
Reaction
Synonyms
AccA3-PccB complex, acetyl-CoA/propionyl-CoA carboxylase, Carboxylase, propional coenzyme A (adenosine triphosphate-hydrolyzing), LA_2736-LA_2735, Pcase, PCC, PccA, PccA-1, PCCase, PccB, PccB-1, pccBC, PccE, Propanoyl-CoA:carbon dioxide ligase, Propionyl coenzyme A carboxylase, Propionyl coenzyme A carboxylase (adenosine triphosphate-hydrolyzing), Propionyl coenzyme A carboxylase (ATP-hydrolyzing), Propionyl-CoA carboxylase, propionyl-coenzyme A carboxylase
ECTree
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Organism
Organism on EC 6.4.1.3 - propionyl-CoA carboxylase
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I3R7G3: biotin carboxylase subunit (PccA), I3R7F1: carboxyltransferase component (PccB), I3R7F2: essential small subunit PccX
UniProt
Q877I4: biotin carboxyl carrier protein of acetyl-CoA carboxylase, Q877I3: carboxyltransferase subunit of acetyl-CoA carboxylase, Q877I5: biotin carboxylase subunit of acetyl-CoA carboxylase
Q877I4; Q877I3; Q877I5
UniProt
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1863, 1867, 1868, 1876, 1880, 1881, 651406, 652691, 653246, 653247, 661263, 662392, 671196, 704970, 706079, 744741
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wild type form. The dcm-1 mutant is deficient in propanoyl-CoA carboxylase
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