1.14.11.18: phytanoyl-CoA dioxygenase

This is an abbreviated version!
For detailed information about phytanoyl-CoA dioxygenase, go to the full flat file.

Word Map on EC 1.14.11.18

Reaction

phytanoyl-CoA
+
2-oxoglutarate
+
O2
=
2-hydroxyphytanoyl-CoA
+
succinate
+
CO2

Synonyms

PAHX, PhyH, Phytanic acid oxidase, phytanoyl-CoA 2-hydroxylase, Phytanoyl-CoA alpha-hydroxylase, phytanoyl-CoA hydroxylase

ECTree

     1 Oxidoreductases
         1.14 Acting on paired donors, with incorporation or reduction of molecular oxygen
             1.14.11 With 2-oxoglutarate as one donor, and incorporation of one atom of oxygen into each donor
                1.14.11.18 phytanoyl-CoA dioxygenase

General Information

General Information on EC 1.14.11.18 - phytanoyl-CoA dioxygenase

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GENERAL INFORMATION
ORGANISM
UNIPROT
COMMENTARY hide
LITERATURE
malfunction
infantile-onset Adult Refsum's disease due to phytanoyl-CoA hydroxylase ((PHYH) c.164delT, p.L55fsX12) mutation. The challenges of a successful pregnancy in a patient with Adult Refsums disease due to phytanoyl-CoA hydroxylase deficiency
additional information
-
role of 2-oxoglutarate during cyanophage infection, overview