1.1.1.254: (S)-carnitine 3-dehydrogenase
This is an abbreviated version!
For detailed information about (S)-carnitine 3-dehydrogenase, go to the full flat file.
Reaction
Synonyms
D(+)-carnitine dehydrogenase, D-carnitine dehydrogenase, dehydrogenase, D-carnitine
ECTree
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Substrates Products
Substrates Products on EC 1.1.1.254 - (S)-carnitine 3-dehydrogenase
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REACTION DIAGRAM
(R)-3-hydroxy-4-trimethylaminobutyrate + NAD+
3-dehydrocarnitine + NADH + H+
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-
-
r
3-hydroxy-2-butanone + NAD+
2,3-butandione + NADH
-
enzyme specific for D-carnitine
-
?
3-dehydrocarnitine + NADH + H+
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D-carnitine dehydrogenase
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r
(S)-3-hydroxy-4-trimethylaminobutyrate + NAD+
3-dehydrocarnitine + NADH + H+
-
D-carnitine dehydrogenase
-
r
(S)-3-hydroxy-4-trimethylaminobutyrate + NAD+
3-dehydrocarnitine + NADH + H+
-
-
-
r
(S)-3-hydroxy-4-trimethylaminobutyrate + NAD+
3-dehydrocarnitine + NADH + H+
-
D-carnitine dehydrogenase
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r
(S)-carnitine + NAD+
3-dehydrocarnitine + NADH + H+
-
substrate is derived as a waste product from chemical production procedures of L(-)-carnitine
formation of poly-beta-hydroxybutyrate as a storage product
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?
DL-4-amino-3-keto-n-butyrate + NADH
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D-carnitine dehydrogenase, less than 20% velocity compared to D-carnitine
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?
DL-4-amino-3-hydroxy-n-butyrate + NAD+
DL-4-amino-3-keto-n-butyrate + NADH
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D-carnitine dehydrogenase
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?
?
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-
initial step of D(+)-carnitine degradation
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-
?
additional information
?
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it is expected that D-carnitine can be converted into L-carnitine by coupling reactions of D-carnitine dehydrogenase and L-carnitine dehydrogenase
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-
?
additional information
?
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it is expected that D-carnitine can be converted into L-carnitine by coupling reactions of D-carnitine dehydrogenase and L-carnitine dehydrogenase
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-
?
additional information
?
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enzyme is induced during growth on D-carnitine
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?