Application | Comment | Organism |
---|---|---|
medicine | plasma biotinidase activity assay for diagnosis and screen newborn infants for biotinidase deficiency, treatment of inborn metabolism errors with large doses of biotin | Homo sapiens |
Inhibitors | Comment | Organism | Structure |
---|---|---|---|
biotin | competitive inhibition at acidic pH, no inhibition at ph 7.4 with p-(N-biotinylamino)benzoic acid as substrate | Homo sapiens | |
biotin | competitive inhibition at acidic pH, no inhibition at ph 7.4 with p-(N-biotinylamino)benzoic acid as substrate | Sus scrofa |
KM Value [mM] | KM Value Maximum [mM] | Substrate | Comment | Organism | Structure |
---|---|---|---|---|---|
0.008 | - |
epsilon-N-biotinyl-L-lysine | - |
Sus scrofa | |
0.01 | - |
epsilon-N-biotinyl-L-lysine | porcine liver | Sus scrofa | |
0.01 | - |
biotinyl-4-aminobenzoic acid | porcine liver, human serum | Homo sapiens | |
0.01 | - |
biotinyl-4-aminobenzoic acid | porcine liver, human serum | Sus scrofa | |
0.016 | - |
epsilon-N-biotinyl-L-lysine | - |
Sus scrofa | |
0.022 | - |
Biotinyl-6-aminoquinoline | human plasma | Homo sapiens | |
0.055 | - |
biotinyl-4-aminobenzoic acid | porcine serum | Sus scrofa |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
biotin amide + H2O | Homo sapiens | - |
? | - |
? | |
biotin amide + H2O | Sus scrofa | - |
? | - |
? | |
epsilon-N-biotinyl-L-lysine + H2O | Homo sapiens | - |
? | - |
? | |
epsilon-N-biotinyl-L-lysine + H2O | Sus scrofa | - |
? | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
human | - |
Sus scrofa | - |
pig | - |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
blood | serum, plasma, leukocytes | Homo sapiens | - |
blood | serum, plasma, leukocytes | Sus scrofa | - |
fibroblast | - |
Homo sapiens | - |
kidney | - |
Homo sapiens | - |
kidney | - |
Sus scrofa | - |
liver | - |
Homo sapiens | - |
liver | - |
Sus scrofa | - |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
biotin amide + H2O | - |
Homo sapiens | ? | - |
? | |
biotin amide + H2O | - |
Sus scrofa | ? | - |
? | |
biotinyl-4-aminobenzoic acid + H2O | - |
Sus scrofa | biotin + 4-aminobenzoic acid | - |
? | |
biotinyl-4-aminobenzoic acid + H2O | colorimetric synthetic substrate | Homo sapiens | biotin + 4-aminobenzoic acid | - |
? | |
biotinyl-6-aminoquinoline + H2O | BAQ, fluorogenic substrate as assay for biotinidase | Homo sapiens | biotin + 6-aminoquinoline | - |
? | |
epsilon-N-biotinyl-L-lysine + H2O | - |
Homo sapiens | biotin + L-lysine | - |
ir | |
epsilon-N-biotinyl-L-lysine + H2O | - |
Sus scrofa | biotin + L-lysine | - |
ir | |
epsilon-N-biotinyl-L-lysine + H2O | - |
Homo sapiens | ? | - |
? | |
epsilon-N-biotinyl-L-lysine + H2O | - |
Sus scrofa | ? | - |
? |