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Literature summary for 3.10.1.1 extracted from

  • Kresse, H.
    Mucopolysaccharidosis III A (sanfilipo A disease): deficiency of a heparin sulfamidase in skin fibroblasts and leucocytes (1973), Biochem. Biophys. Res. Commun., 54, 1111-1118.
    View publication on PubMed

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
heparan sulfate + H2O Mammalia
-
? + sulfate
-
?
heparan sulfate + H2O Homo sapiens
-
? + sulfate
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-
Mammalia
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
fibroblast
-
Homo sapiens
-
leukocyte
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
heparan sulfate + H2O
-
Mammalia ? + sulfate
-
?
heparan sulfate + H2O
-
Homo sapiens ? + sulfate
-
?
heparan sulfate + H2O
-
Homo sapiens ? + sulfate
-
ir

pH Optimum

pH Optimum Minimum pH Optimum Maximum Comment Organism
5
-
-
Homo sapiens