Molecular Weight [Da] | Molecular Weight Maximum [Da] | Comment | Organism |
---|---|---|---|
40000 | - |
1 * 40000, SDS-PAGE | Homo sapiens |
42000 | - |
1 * 42000, SDS-PAGE | Homo sapiens |
Natural Substrates | Organism | Comment (Nat. Sub.) | Natural Products | Comment (Nat. Pro.) | Rev. | Reac. |
---|---|---|---|---|---|---|
additional information | Homo sapiens | third enzyme in the heme biosynthetic pathway | ? | - |
? | |
porphobilinogen | Homo sapiens | - |
? | - |
? |
Organism | UniProt | Comment | Textmining |
---|---|---|---|
Homo sapiens | - |
- |
- |
Purification (Comment) | Organism |
---|---|
2 forms | Homo sapiens |
Source Tissue | Comment | Organism | Textmining |
---|---|---|---|
lymphoblast | - |
Homo sapiens | - |
Specific Activity Minimum [µmol/min/mg] | Specific Activity Maximum [µmol/min/mg] | Comment | Organism |
---|---|---|---|
additional information | - |
- |
Homo sapiens |
0.00117 | - |
- |
Homo sapiens |
0.0128 | - |
40 kDa enzyme form | Homo sapiens |
0.0183 | - |
42 kDa enzyme form | Homo sapiens |
Substrates | Comment Substrates | Organism | Products | Comment (Products) | Rev. | Reac. |
---|---|---|---|---|---|---|
4 porphobilinogen | in the presence of uroporphyrinogen III cosynthase, EC 4.2.1.75 | Homo sapiens | uroporphyrinogen III + 4 NH3 | - |
? | |
4 porphobilinogen + H2O | - |
Homo sapiens | hydroxylmethylbilane + 4 NH3 | - |
? | |
additional information | third enzyme in the heme biosynthetic pathway | Homo sapiens | ? | - |
? | |
porphobilinogen | - |
Homo sapiens | ? | - |
? |
Subunits | Comment | Organism |
---|---|---|
monomer | 1 * 40000, SDS-PAGE | Homo sapiens |
monomer | 1 * 42000, SDS-PAGE | Homo sapiens |
More | the two enzyme forms can each be separated into three differently charged subforms by Mono Q chromatography | Homo sapiens |
Synonyms | Comment | Organism |
---|---|---|
HMB-S | - |
Homo sapiens |
PBGD | - |
Homo sapiens |
porphobilinogen deaminase | - |
Homo sapiens |