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Literature summary for 2.1.4.1 extracted from

  • Verhoeven, N.M.; Schor, D.S.M.; Roos, B.; Battini, R.; Stockler-Ipsiroglu, S.; Salomons, G.S.; Jakobs, C.
    Diagnostic enzyme assay that uses stable-isotope-labeled substrates to detect L-arginine: glycine amidinotransferase deficiency (2003), Clin. Chem., 49, 803-805.
    View publication on PubMed

Protein Variants

Protein Variants Comment Organism
medicine in vitro assay for enzyme activity in lymphocytes based on stable-isotope-labeled substrates L-(guanidino-15N2)arginine and U-(13C,15N)glycine Homo sapiens

Inhibitors

Inhibitors Comment Organism Structure
L-ornithine
-
Homo sapiens

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
lymphoblast
-
Homo sapiens
-
lymphocyte
-
Homo sapiens
-

Specific Activity [micromol/min/mg]

Specific Activity Minimum [µmol/min/mg] Specific Activity Maximum [µmol/min/mg] Comment Organism
additional information
-
in vitro assay for enzyme activity based on stable-isotope-labeled substrates L-(guanidino-15N2)arginine and U-(13C,15N)glycine Homo sapiens

Synonyms

Synonyms Comment Organism
AGAT
-
Homo sapiens