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Literature summary for 1.3.8.6 extracted from

  • Goodman, S.I.; Kratz, L.E.; DiGiulio, K.A.; Biery, B.J.; Goodman, K.E.; Isaya, G.; Frerman, F.E.
    Cloning of glutaryl-CoA dehydrogenase cDNA, and expression of wild type and mutant enzymes in Escherichia coli (1995), Hum. Mol. Genet., 4, 1493-1498.
    View publication on PubMed

Cloned(Commentary)

Cloned (Comment) Organism
wild type and mutant of patient with glutaric acidemia type I Homo sapiens

KM Value [mM]

KM Value [mM] KM Value Maximum [mM] Substrate Comment Organism Structure
0.042
-
human electron-transfer flavoprotein
-
Homo sapiens

Localization

Localization Comment Organism GeneOntology No. Textmining
mitochondrion
-
Homo sapiens 5739
-

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
recombinant enzyme
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
glutaryl-CoA + human electron-transfer flavoprotein
-
Homo sapiens crotonyl-CoA + CO2 + reduced human electron-transfer flavoprotein
-
r

Turnover Number [1/s]

Turnover Number Minimum [1/s] Turnover Number Maximum [1/s] Substrate Comment Organism Structure
3.1
-
human electron-transfer flavoprotein recombinant protein Homo sapiens