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Literature summary for 1.14.14.19 extracted from

  • Tian, Q.; Zhang, Y.; Lu, Z.
    Partial 17alpha-hydroxylase/17,20-lyase deficiency-clinical report of five Chinese 46,XX cases (2008), Gynecol. Endocrinol., 24, 362-367.
    View publication on PubMed

Application

Application Comment Organism
medicine partial 17alpha-hydroxylase/17,20-lyase deficiency is a very rare form of congenital adrenal hyperplasia Homo sapiens

Molecular Weight [Da]

Molecular Weight [Da] Molecular Weight Maximum [Da] Comment Organism
57000
-
-
Homo sapiens

Natural Substrates/ Products (Substrates)

Natural Substrates Organism Comment (Nat. Sub.) Natural Products Comment (Nat. Pro.) Rev. Reac.
pregnenolone + AH2 + O2 Homo sapiens 17,20-lyase activity 17alpha-hydroxypregnenolone + A + H2O
-
?
progesterone + [reduced NADPH-hemoprotein reductase] + O2 Homo sapiens 17,20-lyase activity 17alpha-hydroxyprogesterone + [oxidized NADPH-hemoprotein reductase] + H2O
-
?

Organism

Organism UniProt Comment Textmining
Homo sapiens
-
-
-

Source Tissue

Source Tissue Comment Organism Textmining
adrenal cortex
-
Homo sapiens
-
gonad
-
Homo sapiens
-

Substrates and Products (Substrate)

Substrates Comment Substrates Organism Products Comment (Products) Rev. Reac.
pregnenolone + AH2 + O2 17,20-lyase activity Homo sapiens 17alpha-hydroxypregnenolone + A + H2O
-
?
progesterone + [reduced NADPH-hemoprotein reductase] + O2 17,20-lyase activity Homo sapiens 17alpha-hydroxyprogesterone + [oxidized NADPH-hemoprotein reductase] + H2O
-
?

Synonyms

Synonyms Comment Organism
17alpha-hydroxylase/17,20-lyase
-
Homo sapiens
CYP17
-
Homo sapiens
cytochrome P450 17alpha-hydroxylase
-
Homo sapiens
P45017alpha
-
Homo sapiens