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UDP-galactose + asialo-GM2
UDP + asialo-GM1
-
i.e. Gg3
-
?
UDP-galactose + ganglioside GA2
UDP + ganglioside GA1
UDP-galactose + GD2
UDP + Gd1b
UDPgalactose + N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine
UDP + D-galactosyl-1,3-beta-N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-D-glucosyl-N-acylsphingosine
additional information
?
-
UDP-galactose + ganglioside GA2
UDP + ganglioside GA1
i.e. Cer-Glc-Gal-GalNAc
i.e. Cer-Glc-Gal-GalNAc-Gal
?
UDP-galactose + ganglioside GA2
UDP + ganglioside GA1
i.e. Cer-Glc-Gal-GalNAc
i.e. Cer-Glc-Gal-GalNAc-Gal
?
UDP-galactose + GD2
UDP + Gd1b
i.e. Cer-Glc-Gal-(GalNAc)(NeuNAc2)
i.e. Cer-Glc-Gal-(GalNAc-Gal)(NeuNAc2)
?
UDP-galactose + GD2
UDP + Gd1b
i.e. Cer-Glc-Gal-(GalNAc)(NeuNAc2)
i.e. Cer-Glc-Gal-(GalNAc-Gal)(NeuNAc2)
?
UDPgalactose + N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine
UDP + D-galactosyl-1,3-beta-N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-D-glucosyl-N-acylsphingosine
-
key enzyme in the biosynthesis of the oligodendrocyte- and myelin-specific cerebrosides
-
?
UDPgalactose + N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine
UDP + D-galactosyl-1,3-beta-N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-D-glucosyl-N-acylsphingosine
involved in biosynthesis of gangliosides
i.e. GM1
?
UDPgalactose + N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine
UDP + D-galactosyl-1,3-beta-N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-D-glucosyl-N-acylsphingosine
involved in biosynthesis of gangliosides
i.e. GM1
?
UDPgalactose + N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine
UDP + D-galactosyl-1,3-beta-N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-D-glucosyl-N-acylsphingosine
-
-
-
-
?
UDPgalactose + N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine
UDP + D-galactosyl-1,3-beta-N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-D-glucosyl-N-acylsphingosine
-
key enzyme in the biosynthesis of the oligodendrocyte- and myelin-specific cerebrosides
-
-
?
UDPgalactose + N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine
UDP + D-galactosyl-1,3-beta-N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-D-glucosyl-N-acylsphingosine
-
involved in biosynthesis of gangliosides
-
-
?
UDPgalactose + N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-1,4-beta-D-glucosyl-N-acylsphingosine
UDP + D-galactosyl-1,3-beta-N-acetyl-D-galactosaminyl-(N-acetylneuraminyl)-D-galactosyl-D-glucosyl-N-acylsphingosine
-
key enzyme in the biosynthesis of the oligodendrocyte- and myelin-specific cerebrosides
-
-
?
additional information
?
-
-
mice heterozygous for a non-functional allele of UDPgalactose:ceramide-galactosyltransferase show decreased synthesis of galactosylceramide and sulfatide, which should reduce sulfatide storage and improve pathology in arylsulfatase A-deficient mice. The phenotypic and pathologic improvements in ASA-/- CGT+/- mice are significant but overall minor
-
-
?
additional information
?
-
-
UDPgalactose:ceramide galactosyltransferase activity does not limit total galactosylceramide level. Tight control of UDP-galactose:ceramide galactosyltransferase expression is essential for myelin maintenance
-
-
?