1.3.8.8: long-chain acyl-CoA dehydrogenase
This is an abbreviated version!
For detailed information about long-chain acyl-CoA dehydrogenase, go to the full flat file.
Word Map on EC 1.3.8.8
-
1.3.8.8
-
medium-chain
-
beta-oxidation
-
carnitine
-
acylcarnitine
-
cardiomyopathy
-
cardiac
-
peroxisome
-
triglyceride
-
rhabdomyolysis
-
hypoglycemia
-
acadvl
-
palmitoyltransferase
-
proliferator-activated
-
inborn
-
trifunctional
-
nbs
-
3-hydroxyacyl-coa
-
acidurias
-
myopathic
-
hypoketotic
-
glutaric
-
myoglobinuria
-
dehydrogenase-deficient
-
isovaleryl-coa
-
bezafibrate
-
lchad
-
faods
-
medicine
-
mcadd
- 1.3.8.8
-
medium-chain
-
beta-oxidation
- carnitine
- acylcarnitine
- cardiomyopathy
- cardiac
- peroxisome
- triglyceride
- rhabdomyolysis
- hypoglycemia
- acadvl
- palmitoyltransferase
-
proliferator-activated
-
inborn
-
trifunctional
- nbs
- 3-hydroxyacyl-coa
- acidurias
-
myopathic
-
hypoketotic
-
glutaric
- myoglobinuria
-
dehydrogenase-deficient
- isovaleryl-coa
- bezafibrate
- lchad
-
faods
- medicine
-
mcadd
Reaction
Synonyms
ACAD 9, AcdB, acyl-CoA dehydrogenase 9, BACH, CTE-II, EC 1.3.99.13, EC 1.3.99.3, LCAD, long chain acyl coenzyme A dehydrogenase, long chain acyl-CoA dehydrogenase, long-chain acyl-CoA dehydrogenase, long-chain acyl-CoA hydrolase, long-chain acyl-coenzyme A dehydrogenase, MCAD, medium long-chain acyl-CoA dehydrogenase, More, MTE-II, palmitoyl-CoA dehydrogenase, palmitoyl-coenzyme A dehydrogenase, PtmO4, type-II acyl-CoA thioesterase, very long chain acyl-CoA dehydrogenase, very long-chain acyl-CoA dehydrogenase, very-long-chain acyl-CoA dehydrogenase, very-long-chain acyl-coenzyme A dehydrogenase, VLCAD, VLMCAD
ECTree
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Substrates Products
Substrates Products on EC 1.3.8.8 - long-chain acyl-CoA dehydrogenase
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REACTION DIAGRAM
(R/S)-2-methylpalmitoyl-CoA + electron-transfer flavoprotein
2,3-dehydro-2-methylpalmitoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
(S)-2-methylpentadecanoyl-CoA + electron-transfer flavoprotein
2-methyl-2-pentadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
2,6-dimethylheptanoyl-CoA + oxidized flavin
2,3-dehydro-2,6-dimethylheptanoyl-CoA + reduced flavin
-
specific LCAD substrate
-
-
?
4-cis-7-cis-decadienoyl-CoA + Meldola's Blue
2-trans-4,7-cis,cis-decatrienoyl-CoA + reduced meldola blue
-
-
-
?
4-cis-decenoyl-CoA + Meldola's Blue
2-trans-4-cis-decadienoyl-CoA + reduced meldola blue
-
-
-
?
5-cis-decenoyl-CoA + Meldola's Blue
2-trans-5-cis-decadienoyl-CoA + reduced meldola blue
-
-
-
?
6-cis-decenoyl-CoA + Meldola's Blue
2-trans-6-cis-decadienoyl-CoA + reduced meldola blue
-
-
-
?
arachidonoyl-CoA + acceptor
? + reduced acceptor
-
48.9% activity compared to the wild type enzyme
-
-
?
arachidonoyl-CoA + electron transfer flavoprotein
(2E,5Z,8Z,11Z,14Z)-2,5,8,11,14-eicosapentaenoyl-CoA + reduced electron transfer flavoprotein
-
48.9% activity compared to palmitoyl-CoA
-
-
?
arachidonoyl-CoA + phenazine methosulfate
(2E,5Z,8Z,11Z,14Z)-2,5,8,11,14-eicosapentaenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
butyryl-CoA + electron-transfer flavoprotein
2-butenoyl-CoA + reduced electron-transfer flavoprotein
butyryl-CoA + phenazine methosulfate
2-butenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
cis,cis,cis,cis-4,7,10,13-hexadecatetraenoyl-CoA + Meldola's Blue
2-trans-4,7,10,13-cis,cis,cis,cis-hexadecapentaenoyl-CoA + reduced meldola blue
-
-
-
?
decanoyl-CoA + electron-transfer flavoprotein
2-decenoyl-CoA + reduced electron-transfer flavoprotein
decanoyl-CoA + Meldola's Blue
2-decenoyl-CoA + reduced meldola blue
-
-
trans-isomer
?
decanoyl-CoA + phenazine methosulfate
(2E)-2-decenoyl-CoA + reduced phenazine methosulfate
docosanoyl-CoA + electron-transfer flavoprotein
2-docosenoyl-CoA + reduced electron-transfer flavoprotein
dodecanoyl-CoA + electron-transfer flavoprotein
2-dodecenoyl-CoA + reduced electron-transfer flavoprotein
dodecanoyl-CoA + Meldola's Blue
2-dodecenoyl-CoA + reduced meldola blue
-
-
trans-isomer
?
dodecanoyl-CoA + phenazine methosulfate
(2E)-2-dodecenoyl-CoA + reduced phenazine methosulfate
eicosanoyl-CoA + electron-transfer flavoprotein
trans-2-eicosenoyl-CoA + reduced electron-transfer flavoprotein
eicosanoyl-CoA + phenazine methosulfate
trans-2-eicosenoyl-CoA + reduced phenazine methosulfate
erucoyl-CoA + phenazine methosulfate
(2E,13Z)-2,13-docosadienoyl-CoA + reduced phenazine methosulfate
-
-
-
?
hexanoyl-CoA + electron-transfer flavoprotein
2-hexenoyl-CoA + reduced electron-transfer flavoprotein
hexanoyl-CoA + Meldola's Blue
(2E)-2-hexenoyl-CoA + reduced meldola blue
-
-
trans-isomer
?
lineoyl-CoA + acceptor
2,9,12-octadecatrienoyl-CoA + reduced acceptor
-
12.5% activity compared to the wild type enzyme
-
-
?
linolenoyl-CoA + phenazine methosulfate
(2E,6Z,9Z,12Z)2,6,9,12-octadecatetraenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
linoleoyl-CoA + acceptor
2,9,12-octadecatrienoyl-CoA + reduced acceptor
-
-
-
-
?
linoleoyl-CoA + electron transfer flavoprotein
2,9,12-octadecatrienoyl-CoA + reduced electron transfer flavoprotein
-
12.5% activity compared to palmitoyl-CoA
-
-
?
linoleoyl-CoA + phenazine methosulfate
(2E,9Z,12Z)-2,9,12-octadecatrienoyl-CoA + reduced phenazine methosulfate
-
-
-
?
myristoyl-CoA + acceptor
? + reduced acceptor
-
51.1% activity compared to the wild type enzyme
-
-
?
myristoyl-CoA + acceptor
trans(2)-tetradecenoyl-CoA + reduced acceptor
-
-
-
-
?
myristoyl-CoA + electron transfer flavoprotein
? + reduced electron transfer flavoprotein
-
51.1% activity compared to palmitoyl-CoA
-
-
?
octanoyl-CoA + electron-transfer flavoprotein
2-octenoyl-CoA + reduced electron-transfer flavoprotein
octanoyl-CoA + Meldola's Blue
(2E)-2-octenoyl-CoA + reduced meldola blue
-
-
trans-isomer
?
oleoyl-CoA + acceptor
(2E,9Z)-2,9-octadecadienoyl-CoA + reduced acceptor
-
-
-
-
?
oleoyl-CoA + electron transfer flavoprotein
2,9-octadecadienoyl-CoA + reduced electron transfer flavoprotein
-
40.8% activity compared to palmitoyl-CoA
-
-
?
oleoyl-CoA + phenazine methosulfate
(2E,9Z)-2,9-octadecadienoyl-CoA + reduced phenazine methosulfate
-
-
-
?
omega-phenyldecanoyl-CoA + phenazine methosulfate
10-phenyl-2-decenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
omega-phenyldodecanoyl-CoA + phenazine methosulfate
12-phenyl-2-dodecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
palmitoleoyl-CoA + acceptor
(2E,9Z)-2,9-hexadecadienoyl-CoA + reduced acceptor
-
34.8% activity compared to the wild type enzyme
-
-
?
palmitoleoyl-CoA + electron transfer flavoprotein
(2E,9Z)-2,9-hexadecadienoyl-CoA + reduced electron transfer flavoprotein
-
34.8% activity compared to palmitoyl-CoA
-
-
?
palmitoleoyl-CoA + phenazine methosulfate
(2E,9Z)-2,9-hexadecadienoyl-CoA + reduced phenazine methosulfate
-
-
-
?
palmitoyl-CoA + acceptor
2,3-unsaturated-palmitoyl-CoA + reduced acceptor
-
-
-
?
palmitoyl-CoA + electron transfer flavoprotein
2-hexadecenoyl-CoA + reduced electron transfer flavoprotein
-
100% activity with palmitoyl-CoA
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
(2E)-2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
palmitoyl-CoA + electron-transfer flavoprotein
2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
palmitoyl-CoA + Meldola's Blue
2-hexadecenoyl-CoA + reduced meldola blue
-
-
trans-isomer
?
palmitoyl-CoA + phenazine methosulfate
2-hexadecenoyl-CoA + reduced phenazine methosulfate
stearoyl-CoA + acceptor
2-octadecenoyl-CoA + reduced acceptor
-
39% activity compared to the wild type enzyme
-
-
?
stearoyl-CoA + electron transfer flavoprotein
2-octadecenoyl-CoA + reduced electron transfer flavoprotein
-
39.0% activity compared to palmitoyl-CoA
-
-
?
stearoyl-CoA + electron-transfer flavoprotein
2-octadecenoyl-CoA + reduced electron-transfer flavoprotein
stearoyl-CoA + Meldola's Blue
2-octadecenoyl-CoA + reduced meldola blue
-
-
trans-isomer
?
tetradecanoyl-CoA + electron-transfer flavoprotein
2-tetradecenoyl-CoA + reduced electron-transfer flavoprotein
tetradecanoyl-CoA + Meldola's Blue
2-tetradecenoyl-CoA + reduced meldola blue
-
-
trans-isomer
?
tetradecanoyl-CoA + phenazine methosulfate
2-tetradecenoyl-CoA + reduced phenazine methosulfate
acyl-CoA + acceptor
2,3-dehydroacyl-CoA + reduced acceptor
-
-
-
-
?
2-butenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
butyryl-CoA + electron-transfer flavoprotein
2-butenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
2-decenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
decanoyl-CoA + electron-transfer flavoprotein
2-decenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
decanoyl-CoA + electron-transfer flavoprotein
2-decenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
decanoyl-CoA + electron-transfer flavoprotein
2-decenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
decanoyl-CoA + electron-transfer flavoprotein
2-decenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
decanoyl-CoA + electron-transfer flavoprotein
2-decenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
(2E)-2-decenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
decanoyl-CoA + phenazine methosulfate
(2E)-2-decenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
decanoyl-CoA + phenazine methosulfate
(2E)-2-decenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
decanoyl-CoA + phenazine methosulfate
(2E)-2-decenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
decanoyl-CoA + phenazine methosulfate
(2E)-2-decenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
decanoyl-CoA + phenazine methosulfate
(2E)-2-decenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
decanoyl-CoA + phenazine methosulfate
(2E)-2-decenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
decanoyl-CoA + phenazine methosulfate
(2E)-2-decenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
decanoyl-CoA + phenazine methosulfate
(2E)-2-decenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
decanoyl-CoA + phenazine methosulfate
(2E)-2-decenoyl-CoA + reduced phenazine methosulfate
-
trans-isomer
-
?
2-docosenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
docosanoyl-CoA + electron-transfer flavoprotein
2-docosenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
2-docosenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
docosanoyl-CoA + phenazine methosulfate
2-docosenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
2-dodecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
dodecanoyl-CoA + electron-transfer flavoprotein
2-dodecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
dodecanoyl-CoA + electron-transfer flavoprotein
2-dodecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
dodecanoyl-CoA + electron-transfer flavoprotein
2-dodecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
dodecanoyl-CoA + electron-transfer flavoprotein
2-dodecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
dodecanoyl-CoA + electron-transfer flavoprotein
2-dodecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
(2E)-2-dodecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
dodecanoyl-CoA + phenazine methosulfate
(2E)-2-dodecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
dodecanoyl-CoA + phenazine methosulfate
(2E)-2-dodecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
dodecanoyl-CoA + phenazine methosulfate
(2E)-2-dodecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
dodecanoyl-CoA + phenazine methosulfate
(2E)-2-dodecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
dodecanoyl-CoA + phenazine methosulfate
(2E)-2-dodecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
dodecanoyl-CoA + phenazine methosulfate
(2E)-2-dodecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
dodecanoyl-CoA + phenazine methosulfate
(2E)-2-dodecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
dodecanoyl-CoA + phenazine methosulfate
(2E)-2-dodecenoyl-CoA + reduced phenazine methosulfate
-
trans-isomer
-
?
trans-2-eicosenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
eicosanoyl-CoA + electron-transfer flavoprotein
trans-2-eicosenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
eicosanoyl-CoA + electron-transfer flavoprotein
trans-2-eicosenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
trans-2-eicosenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
eicosanoyl-CoA + phenazine methosulfate
trans-2-eicosenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
eicosanoyl-CoA + phenazine methosulfate
trans-2-eicosenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
2-hexenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
hexanoyl-CoA + electron-transfer flavoprotein
2-hexenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
hexanoyl-CoA + electron-transfer flavoprotein
2-hexenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
hexanoyl-CoA + electron-transfer flavoprotein
2-hexenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
2-hexenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
hexanoyl-CoA + phenazine methosulfate
2-hexenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
hexanoyl-CoA + phenazine methosulfate
2-hexenoyl-CoA + reduced phenazine methosulfate
-
trans-isomer
-
?
2-dodecenoyl-CoA + reduced acceptor
enzyme shows preference for long-chain fatty acids
-
-
?
lauroyl-CoA + acceptor
2-dodecenoyl-CoA + reduced acceptor
enzyme shows preference for long-chain fatty acids
-
-
?
2-octenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
octanoyl-CoA + electron-transfer flavoprotein
2-octenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
octanoyl-CoA + electron-transfer flavoprotein
2-octenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
octanoyl-CoA + electron-transfer flavoprotein
2-octenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
octanoyl-CoA + electron-transfer flavoprotein
2-octenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
octanoyl-CoA + electron-transfer flavoprotein
2-octenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
2-octenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
octanoyl-CoA + phenazine methosulfate
2-octenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
octanoyl-CoA + phenazine methosulfate
2-octenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
octanoyl-CoA + phenazine methosulfate
2-octenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
octanoyl-CoA + phenazine methosulfate
2-octenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
octanoyl-CoA + phenazine methosulfate
2-octenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
octanoyl-CoA + phenazine methosulfate
2-octenoyl-CoA + reduced phenazine methosulfate
-
trans-isomer
-
?
2,9-octadecadienoyl-CoA + reduced acceptor
-
-
-
-
?
oleoyl-CoA + acceptor
2,9-octadecadienoyl-CoA + reduced acceptor
-
40.8% activity compared to the wild type enzyme
-
-
?
(2E)-2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
(2E)-2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
(2E)-2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
100% activity
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
(2E)-2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
(2E)-2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
enzyme does not affect all acyl-CoA utilizing cellular processes
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
(2E)-2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
-
?
2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
palmitoyl-CoA + electron-transfer flavoprotein
2-hexadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
2-hexadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
palmitoyl-CoA + phenazine methosulfate
2-hexadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
palmitoyl-CoA + phenazine methosulfate
2-hexadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
palmitoyl-CoA + phenazine methosulfate
2-hexadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
palmitoyl-CoA + phenazine methosulfate
2-hexadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
palmitoyl-CoA + phenazine methosulfate
2-hexadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
palmitoyl-CoA + phenazine methosulfate
2-hexadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
palmitoyl-CoA + phenazine methosulfate
2-hexadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
palmitoyl-CoA + phenazine methosulfate
2-hexadecenoyl-CoA + reduced phenazine methosulfate
-
trans-isomer
-
?
platensimycin ML1 + electron-transfer flavoprotein
?
-
-
-
?
2-octadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
stearoyl-CoA + electron-transfer flavoprotein
2-octadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
stearoyl-CoA + electron-transfer flavoprotein
2-octadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
stearoyl-CoA + electron-transfer flavoprotein
2-octadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
stearoyl-CoA + electron-transfer flavoprotein
2-octadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
stearoyl-CoA + electron-transfer flavoprotein
2-octadecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
2-octadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
stearoyl-CoA + phenazine methosulfate
2-octadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
stearoyl-CoA + phenazine methosulfate
2-octadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
stearoyl-CoA + phenazine methosulfate
2-octadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
stearoyl-CoA + phenazine methosulfate
2-octadecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
stearoyl-CoA + phenazine methosulfate
2-octadecenoyl-CoA + reduced phenazine methosulfate
-
trans-isomer
-
?
2-tetradecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
tetradecanoyl-CoA + electron-transfer flavoprotein
2-tetradecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
tetradecanoyl-CoA + electron-transfer flavoprotein
2-tetradecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
tetradecanoyl-CoA + electron-transfer flavoprotein
2-tetradecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
tetradecanoyl-CoA + electron-transfer flavoprotein
2-tetradecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
tetradecanoyl-CoA + electron-transfer flavoprotein
2-tetradecenoyl-CoA + reduced electron-transfer flavoprotein
-
-
-
?
2-tetradecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
tetradecanoyl-CoA + phenazine methosulfate
2-tetradecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
tetradecanoyl-CoA + phenazine methosulfate
2-tetradecenoyl-CoA + reduced phenazine methosulfate
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tetradecanoyl-CoA + phenazine methosulfate
2-tetradecenoyl-CoA + reduced phenazine methosulfate
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-
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?
tetradecanoyl-CoA + phenazine methosulfate
2-tetradecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
tetradecanoyl-CoA + phenazine methosulfate
2-tetradecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
tetradecanoyl-CoA + phenazine methosulfate
2-tetradecenoyl-CoA + reduced phenazine methosulfate
-
-
-
?
tetradecanoyl-CoA + phenazine methosulfate
2-tetradecenoyl-CoA + reduced phenazine methosulfate
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trans-isomer
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enzyme deficiency may ba a cause of autism, physiological alterations in case of enzyme deficiency are in TCA energy metabolism, ammonia detoxification, and synthesis of omega-3 DHA, and elevated acyl-carnitine levels, the mitochondrial enzyme is responsible for beta-oxidation of branched and unsaturated fatty acids with preference for long-chain fatty acids
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additional information
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enzyme has broad substrate specificity with preference for medium- and long-chain fatty acids, overview
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additional information
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CTE-II highly specific for the hydrolysis of acyl-CoAs
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additional information
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catalyses the initial step of mitochondrial beta-oxidation of long-chain fatty acids with a chain length of 14 to 20 carbons
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additional information
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reaction with acyl-CoA in absence of an electron acceptor, half-reaction, suggests the catalytic base and flavin adenine dinucleotide are located in a pocket
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additional information
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enzyme-catalyzed proton-deuteron exchange experiments in absence of an electron acceptor, deuterium atom replaces hydrogen from C-2 giving experimental evidence for the initial C-2 proton abstraction
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