1.3.8.4: isovaleryl-CoA dehydrogenase
This is an abbreviated version!
For detailed information about isovaleryl-CoA dehydrogenase, go to the full flat file.
Word Map on EC 1.3.8.4
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1.3.8.4
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acidemia
-
acyl-coa
-
inborn
-
3-methylcrotonyl-coa
-
isovalerylglycine
-
medium-chain
-
lethargy
-
flavoenzyme
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isobutyryl-coa
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acylcarnitine
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isovalerylcarnitine
-
flavoprotein:ubiquinone
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glutaryl-coa
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2-methylbutyryl-coa
-
3-hydroxyisovaleric
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octanoyl-coa
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sweaty
-
diagnostics
-
medicine
- 1.3.8.4
-
acidemia
- acyl-coa
-
inborn
- 3-methylcrotonyl-coa
-
isovalerylglycine
-
medium-chain
-
lethargy
-
flavoenzyme
- isobutyryl-coa
- acylcarnitine
- isovalerylcarnitine
-
flavoprotein:ubiquinone
- glutaryl-coa
- 2-methylbutyryl-coa
-
3-hydroxyisovaleric
- octanoyl-coa
-
sweaty
- diagnostics
- medicine
Reaction
Synonyms
acyl-CoA dehydrogenase, EC 1.3.99.10, i3VD, iso(3)valeryl-CoA dehydrogenase, isovaleric-CoA dehydrogenase, isovaleroyl-coenzyme A dehydrogenase, isovaleryl-coenzyme A dehydrogenase, IVD, IVDH, LiuA, Pden_3633, SBCAD, short/branched chain acyl-CoA dehydrogenase
ECTree
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Turnover Number
Turnover Number on EC 1.3.8.4 - isovaleryl-CoA dehydrogenase
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0.3
(S)-2-methylbutyryl-CoA
wild-type enzyme and mutant IVD G375E, pH 7.4, 37°C
0.133
butyryl-CoA
-
using recombinant enzyme, electron acceptor: electron-transferring flavoprotein
0.533
hexanoyl-CoA
-
using recombinant enzyme, electron acceptor: electron-transferring flavoprotein
0.267
valeryl-CoA
-
using recombinant enzyme, electron acceptor: electron-transferring flavoprotein
0.283
isovaleryl-CoA
purified V342A mutant, electron acceptor: dichlorophenol indophenol
0.733
isovaleryl-CoA
purified R382L mutant, electron acceptor: dichlorophenol indophenol
0.817
isovaleryl-CoA
purified V342A mutant, electron acceptor: electron-transferring flavoprotein
2
isovaleryl-CoA
purified R382L mutant, electron acceptor: electron-transferring flavoprotein
2.2
isovaleryl-CoA
purified A282V mutant, electron acceptor: electron-transferring flavoprotein
2.37
isovaleryl-CoA
-
using recombinant enzyme, electron acceptor: electron-transferring flavoprotein
2.82
isovaleryl-CoA
purified A282V mutant, electron acceptor: dichlorophenol indophenol
8.8
isovaleryl-CoA
purified wild-type enzyme, electron acceptor: electron-transferring flavoprotein
10
isovaleryl-CoA
purified wild-type enzyme, electron acceptor: dichlorophenol indophenol